Subjects |
19 |
年龄(范围) |
39.4±14.2(18.1–63.1) |
女性 |
17 (89) |
特发性/可遗传/与厌食症相关的PAH |
9/10/0 |
BMPR2mutation carrier n/n tested (%) |
10/13(77) |
NYHA functional class III/IV |
8(42)/11(58) |
步行6分钟M |
215±174 |
血液动力学 |
|
Right atrial pressure mmHg |
12.2±5.2 |
Mean pulmonary arterial pressure mmHg |
67.7±15.8 |
Pulmonary capillary wedge pressure mmHg |
8.3±3.4 |
Cardiac output L·min−1 |
2.83±0.77 |
Cardiac index L·min−1·m−2 |
1.64±0.34 |
Pulmonary vascular resistance dyn·s·cm−5 |
1807±722 |
Mean blood pressure mmHg |
91.7±12.2 |
Heart rate beats per min |
92.3±10.7 |
Mixed venous oxygen saturation % |
50.1±9.0 |