|
Pvod. |
iPah. |
p值 |
临床特征 |
|
|
|
Subjects n |
8. |
11. |
|
Age yrs |
52±17. |
44±10. |
ns. |
Sex male/female |
5/3 |
3/8 |
ns. |
Smoking n (%) |
6(75) |
4(36) |
ns. |
Raynaud's phenomenon n (%) |
1(12.5) |
1(9) |
ns. |
NYHA functional class n (%) |
|
|
|
I–II |
2(25) |
2(18) |
ns. |
III–IV |
6(75) |
9(82) |
ns. |
Right-ventricular failure n (%) |
8(100) |
5(45) |
<0.05 |
Digital clubbing n (%) |
2(25) |
0. |
ns. |
Crackles n (%) |
2(25) |
0. |
ns. |
Baseline 6-MWD distance m |
216±138. |
372±82. |
0.02 |
血管正动参数 |
|
|
|
Mean right-atrial pressure mmHg |
10±5. |
10±5. |
ns. |
Mean pulmonary artery pressure mmHg |
59±8. |
58±10. |
ns. |
Mean PAWP mmHg |
7±3. |
9±3. |
ns. |
Cardiac index L·min-1·M.-2 |
2.1±0.7 |
2.5±0.6 |
ns. |
Mixed venous oxygen saturation % |
57±8. |
66±10. |
ns. |
Total pulmonary resistance IU·m-2 |
31±15. |
25±10. |
ns. |
肺功能测试 |
|
|
|
P.A,O.2mmhg. |
58±11. |
78±14. |
0.007 |
P.A,CO.2mmhg. |
32±6. |
31±4. |
ns. |
FEV1%pred. |
90±12. |
98±21. |
ns. |
VC % pred |
89±13. |
97±17. |
ns. |
TLC % pred |
93±15. |
97±15. |
ns. |
D.L,CO./V.一种%pred. |
37±9. |
62±16. |
0.008 |
支气管肺泡灌洗 |
|
|
|
Volume mL |
55±19. |
64±36. |
ns. |
Cells per mL |
410250±366500. |
204300±158200. |
ns. |
Lymphocytes % |
9±8. |
11±7. |
ns. |
Neutrophils % |
1±1 |
1±1 |
ns. |
Macrophages % |
90±7. |
88±7. |
ns. |
Haemosiderin-laden macrophages % |
40±37. |
3±6. |
0.004. |
Golde score |
81±88. |
4±10. |
0.002 |