抽象的
肺静脉闭塞性疾病(PVOD)是肺动脉高血压影响主要毛细管柱肺血管一种罕见病因。与PVOD主要关心的是可用的治疗反应差和肺水肿的连续静脉注射依前列醇的风险。
本作者假设,肺泡出血可能是肺静脉闭塞性疾病的特征,如与其他形式的肺动脉高压相比该主要涉及预毛细管肺动脉。
This paper reports a series of 19 patients with either PVOD (n = 8) or idiopathic pulmonary arterial hypertension (IPAH; n = 11) who underwent bronchoalveolar lavage. Cytological analyses were performed and differential counts were made on Perls-stained preparations. The Golde score was used to assess alveolar haemorrhage. As compared with IPAH, PVOD was characterised by a higher percentage of haemosiderin-laden macrophages (40±37相对3±6%),导致升高的金果得分(81±88相对4±10)。
得出的结论是隐匿性肺泡出血是肺静脉闭塞性疾病的一个共同特征。检测隐匿性肺泡出血可能是肺静脉闭塞病的诊断方法的兴趣。
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