抽象的
慢性,主要血管血栓栓塞肺动脉高压(CTEPH)是一种罕见的病症,过去是一种尸检的好奇心。诊断方法的进步,手术技术和术后管理转化为潜在可固化的肺动脉高血压形式。主要的症状是劳累的未解释的呼吸困难。在患者中,应考虑CTeph。沿诊断路径存在许多陷阱。灌注肺扫描指向诊断,但往往低估中枢动脉阻塞的程度。肺血管造影是关键的诊断程序,但血栓组织的许多模式 - 重新定化需要一个经验基础进行适当的解释。选择外科患者的标准正在不断发展,但是对手术的血栓可行性保证至关重要。外科血栓栓塞术与急性肺栓塞不相似。识别血栓(与正常内膜),细致的解剖和无流动外科手术领域对于充分恢复肺血管通畅是必不可少的。 Multiple complications may arise postoperatively, and detailed attention to these is required for patient survival. With a co-ordinated, multi-specialty team effort, however, haemodynamic and clinical outcomes have been rewarding and persist long-term. Surgical mortality should steadily decline with such a co-ordinated effort, as well as earlier diagnosis and advances in surgical and postoperative management techniques.