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[(were)-282.5(noted)-279.7(in)-277.1(all)-280.6(patients.)-283.1(The)-280(age)-276.3(at)-277.5(o)-6.5(nset)-274.5(o)-6.5(f)-275.5(respirato)-11.1(ry)]TJ 0 -1.0528 TD [(symp)-7.4(toms)-322.7(was)-320.8(2\26162)-321.7(yrs.)-318.4(The)-6.8(re)-316.5(was)-326.5(a)-314.2(hist)-9(ory)-316.9(of)-321.8(chroni)-9(c)]TJ 25.1977 26.9163 TD [(pan)-8.4(sinusitis)-230.5(in)-231.5(all)-229.4(patients,)-231.9(otitis)-231.5(medi)-9(a)-223.1(i)0(n)-231.5(five)-229.4(out)-226.6(of)-230.7(eight)]TJ 0 -1.0471 TD [(pati)-8.2(ents,)-246.4(infertilit)-14.1(y)-239.8(i)0(n)-242.9(two)-247.6(out)-243.7(of)-230.7(four)-245.2(marr)-9.8(ied)-244.1(patients)-248.6(and)]TJ 0 -1.0528 TD [(sit)-8.2(us)-361.2(in)]TJ /F5 1 Tf 2.9477 0 TD (versus)Tj /F4 1 Tf 2.8965 0 TD [(in)-362.4(all)-366(patients.)-368.4(The)-365.3(mean)-365.5(sputum)-364.1(produc-)]TJ -5.8442 -1.0471 TD [(tion)-491.5(was)-491.5(68)-485.2(g)]TJ /F9 1 Tf 6.0491 0.1992 TD (.)Tj /F4 1 Tf 0.2675 -0.1992 TD 0.0065 Tc [(da)6.5(y)]TJ 7.472 0 0 6.641 386.646 492.151 Tm 0 Tc (-1)Tj 9.963 0 0 9.963 392.768 487.729 Tm [(.)-484.1(P)0(h)-6.4(ysical)-489.3(signs)-492.3(of)-486.8(wheezing)-491.6(and/)]TJ -8.3765 -1.0528 TD [(or)-361.6(c)-6.9(oarse)-360.2(c)-6.9(rackles)-364.5(wer)-8.2(e)-359.7(audible)-369.4(upon)-361.6(aescul)-9.4(ation)-361.8(of)-361.6(the)]TJ 0 -1.0471 TD [(che)-8.8(st)-500.2(in)-504.7(all)-502.5(patients.)-510.7(Exami)-8.2(nation)-504.8(of)-503.9(sputu)-7.4(m)-499(reveal)-9.8(ed)]TJ /F5 1 Tf 0 -1.0527 TD [(Haem)-11.3(ophilus)-216.2(influenz)-9.1(ae)]TJ /F4 1 Tf 9.8162 0 TD (and/or)Tj /F5 1 Tf 2.7485 0 TD [(Pseudom)-9.3(onas)-209.1(aerugi)-8.5(nosa)]TJ /F4 1 Tf -12.5647 -1.0471 TD [(superi)-10.1(nfect)-8.6(ion)-494.1(in)-493.3(all)-496.8(patients.)-499.3(Quinolo)-8.3(ne)-491.3(\(ofl)-8.6(oxacin)-497.2(or)]TJ 0 -1.0528 TD [(levof)-8.2(loxaci)-10.2(n\))-395.8(and)-395.3(macr)-8.6(olide)-395.9(\(eryt)-9.8(hromycin)-400.6(or)-395.8(clari)-11(thro-)]TJ 0 -1.0471 TD [(myci)-9(n\))-361.6(were)-362.2(effective)-357.9(for)-358.3(treat)-11(ment)-361.8(of)-361.6(superinfect)-13.1(ion)-357.5(in)]TJ 0 -1.0528 TD [(most)-328.4(of)-327.5(the)-323.7(patie)-9.4(nts.)-324.9(One)-325.3(patient)-332(\(3\))-324.2(died)-324.5(of)-327.5(progre)-8.2(ssive)]TJ 0 -1.0471 TD [(respi)-9.4(ratory)-448.7(failure)-452.3(38)-439.7(y)-6.5(r)0(s)-442.5(after)-448.4(the)-443.2(onset)-451.7(of)-441.3(respi)-9.4(ratory)]TJ 0 -1.0528 TD [(symp)-7.4(toms.)]TJ /F5 1 Tf 0 -3.1184 TD [(Rad)-6.4(iogra)-7.4(phy)-332.7(images)]TJ /F4 1 Tf 1.0015 -1.747 TD [(Co)16.5(nv)15.5(en)20.8(ti)16.5(on)15.5(al)-522.2(ch)15.1(es)19.6(t)-532.4(r)0(a)13.5(d)0(i)18.9(o)0(g)15.5(r)0(a)19.2(p)0(h)21.2(s)-536.9(sh)20(ow)17.3(ed)-525.5(de)15.1(xt)18.9(ro)19.6(ca)14.7(rd)19.6(ia)]TJ -1.0015 -1.0527 TD [(an)15.1(d)-382(b)0(r)14(o)0(n)21.2(c)0(h)15.1(i)0(e)18.4(c)0(t)18.5(a)0(s)19.6(i)0(s)-375(i)0(n)-373.8(a)0(l)12.8(l)-384.4(pa)20.8(ti)16.5(en)20.8(ts)12(.)-381.6(C)11.6(he)15.1(st)-375(C)11.6(T)-323.6(sh)20(ow)17.3(ed)-377.5(di)18.9(f-)]TJ 0 -1.0471 TD [(fu)13.9(se)-344.6(ce)20.4(nt)13.2(ri)17.3(lo)18.8(bu)21.2(la)12.8(r)-349.5(s)0(m)11.2(a)0(l)18.4(l)-350.3(no)15.5(du)21.2(le)12.8(s)-354.8(u)0(p)-343(t)0(o)-345.3(2)-353.6(mm)-343.6(in)-345.3(di)18.8(am)12(et)18.5(er)]TJ 0 -1.0527 TD [(th)13.2(ro)19.6(ug)15.5(ho)21.2(ut)-220.2(bo)21.2(th)-220.2(lu)18.8(ng)15.5(s)-223.9(i)0(n)-220.2(s)0(i)17.7(x)-228.4(ou)21.2(t)-230.8(o)0(f)-219.4(e)0(i)18.4(g)0(h)21.2(t)-230.8(pa)20.8(ti)16.5(en)15.1(ts)17.7(.)-222.3(B)0(r)14.9(o)0(n)15.5(c)0(h)20.8(i)0(-)]TJ 0 -1.0471 TD [(ec)14.7(ta)18.4(si)17.7(s)-371.8(a)0(n)15.1(d)-370.7(ce)14.7(nt)18.9(ri)17.3(lo)18.9(bu)15.5(l)13.9(a)0(r)-367.7(s)0(m)16.9(a)0(l)18.5(l)-373(no)15.5(du)21.2(le)18.4(s)-371.8(w)0(e)16.9(r)0(e)-367.7(l)0(o)18.9(c)0(a)20.4(l)0(i)16.5(z)0(e)14.7(d)-370.7(to)]TJ 0 -1.0527 TD [(th)13.2(e)-257.2(m)0(i)15.7(d)0(d)15.5(l)0(e)18.4(,)-256.5(th)18.9(e)-262.9(l)0(i)16.5(n)0(g)21.2(u)0(l)13.2(a)-257.2(an)15.1(d)-256.8(l)0(o)18.9(w)0(e)16.9(r)-264.1(lo)18.8(be)15.1(s)-258(i)0(n)-248.6(a)0(l)12.8(l)-259.2(pa)20.8(ti)16.5(en)15.1(ts)17.7(.)-256.5(H)0(y)17.3(-)]TJ 0 -1.0471 TD [(pe)15.1(ri)17.3(nf)19.6(la)12.8(ti)22.2(on)-314.5(wa)16.9(s)-320.6(n)0(o)21.2(t)0(e)18.4(d)-325.1(i)13.9(n)-325.1(fo)19.6(ur)-310.4(ou)15.5(t)-316.1(o)0(f)-310.4(e)0(i)12.8(g)0(h)21.2(t)-321.8(pa)20.8(ti)16.5(en)15.1(ts)17.7(,)-319.1(t)0(r)17.3(a)0(m)17.7(-)]TJ 0 -1.0528 TD [(li)16.5(ne)15.1(s)-286.5(i)0(n)-282.7(s)0(i)17.7(x)-285.3(ou)15.5(t)-287.7(o)0(f)-282(e)0(i)18.5(g)0(h)21.2(t)-293.4(pa)20.8(ti)16.5(en)15.1(t)13.9(s)0(,)-281.2(a)0(n)15.1(d)-285.3(at)18.5(el)12.8(ec)20.4(ta)18.4(si)17.7(s)-292.2(o)0(f)-276.3(t)0(h)13.2(e)-285.7(le)18.4(ft)]TJ 0 -1.0471 TD [(mi)15.7(dd)15.5(le)-368.5(lo)18.9(be)-371.8(an)20.8(d)-382(p)0(n)21.2(e)0(u)15.1(m)0(o)18.1(n)0(i)18.9(a)-376.7(in)-373.8(tw)20.6(o)-382(o)0(u)21.2(t)-378.7(of)-373(ei)18.4(gh)21.2(t)-378.7(p)0(a)15.1(t)0(i)16.5(e)0(n)20.8(t)0(s)]TJ 0 -1.0528 TD [(\(t)17.3(ab)15.1(le)-317.3(2\).)]TJ ET 1 i 58.28 768.302 478.205 -0.51 re f 58.28 732.926 478.205 -0.51 re f 58.28 574.526 478.205 -0.51 re f BT /F3 1 Tf 8.966 0 0 8.966 58.28 772.667 Tm [(Table)-331.9(1.)-336.7(\261)-333.2(Clinical)-334(features)-336(of)-330.4(the)-334.8(study)-333.8(patients)-330.9(with)-336.5(Kartagener)]TJ /F2 1 Tf 28.7945 0 TD (')Tj /F3 1 Tf 0.2213 0 TD [(s)-328.3(syndrome)]TJ /F4 1 Tf -29.0158 -1.7135 TD [(Patient)-1013.4(Age)]TJ 3.9708 -1.0496 TD (yrs)Tj 2.1245 1.0496 TD [(Sex)-1008.5(SI)-1787.9(Respiratory)]TJ 5.6147 -1.0496 TD (symptom)Tj -1.1444 -1.0559 TD [(\(onset)-336.4(age)-333.1(yrs\))]TJ 7.5179 2.1055 TD (Chronic)Tj -0.7398 -1.0496 TD (pansinusitis)Tj 5.482 1.0496 TD (Otitis)Tj -0.1138 -1.0496 TD (media)Tj 3.1109 1.0496 TD (Infertility)Tj 0.0253 -1.0496 TD (\(married\))Tj 5.0899 1.0496 TD (Situs)Tj -0.6639 -1.0496 TD (inversus)Tj 4.6031 1.0496 TD (Sputum)Tj -0.607 -1.0496 TD (production)Tj 0.7398 -1.0559 TD (g)Tj /F9 1 Tf 0.4995 0.2213 TD (.)Tj /F4 1 Tf 0.2719 -0.2213 TD (day)Tj 6.725 0 0 5.977 391.975 742.393 Tm (-1)Tj 8.966 0 0 8.966 421.342 757.304 Tm (Sputum)Tj 0.177 -1.0496 TD (culture)Tj 6.5821 1.0496 TD [(T)34.9(reatment)]TJ -47.2511 -4.1099 TD [(1)-3578.3(3)0(5)-1491.2(F)-1661(0)-1194.5(Cough,)-327.5(sputum)]TJ 12.9873 -1.0559 TD (\(9\))Tj 6.4114 1.0559 TD [(+)-3800.8(-)-2491.7(+)-329.5(\(Y\))-2817.4(+)-3465.7(100)]TJ /F5 1 Tf 19.8666 0 TD [(P)123.5(.)-331.7(aeruginosa)]TJ 0.0822 -1.0559 TD [(H.)-334.5(influenzae)]TJ /F4 1 Tf 6.1522 1.0559 TD [(OFLX,)-332(EM,)-334.8(CAM)]TJ -45.4997 -2.1118 TD [(2)-3578.3(4)0(1)-1320.5(M)-1498.7(0)-1194.5(Cough,)-327.5(sputum)]TJ 12.7407 -1.0559 TD (\(30\))Tj 6.658 1.0559 TD [(+)-3800.8(-)-2491.7(+)-329.5(\(Y\))-2817.4(+)-3712.3(7)0(0)]TJ /F5 1 Tf 19.8666 0 TD [(P)123.5(.)-331.7(aeruginosa)]TJ /F4 1 Tf 7.6634 0 TD [(OFLX,)-332(EM)]TJ -46.9286 -2.1055 TD [(3)-3578.3(5)0(0)-1491.2(F)-1661(0)-1194.5(Cough,)-327.5(sputum)]TJ 12.7407 -1.0559 TD (\(12\))Tj 6.658 1.0559 TD [(+)-3680.7(+)-2492(-)-329.3(\(Y\))-2937.5(+)-3712.3(8)0(0)]TJ /F5 1 Tf 19.8666 0 TD [(P)123.5(.)-331.7(aeruginosa)]TJ /F4 1 Tf 7.6634 0 TD [(OFLX,)-332(EM)]TJ -46.9286 -2.1119 TD [(4)-3578.3(7)0(2)-1320.5(M)-1498.7(0)-1194.5(Cough,)-327.5(sputum)]TJ 12.7407 -1.0559 TD (\(62\))Tj 6.658 1.0559 TD [(+)-3680.7(+)-2492(-)-329.3(\(Y\))-2937.5(+)-3712.3(3)0(0)]TJ /F5 1 Tf 19.8666 0 TD [(P)123.5(.)-331.7(aeruginosa)]TJ 0.0822 -1.0559 TD [(H.)-334.5(influenzae)]TJ /F4 1 Tf 7.2271 1.0559 TD [(L)79.2(VFX,)-335.3(CAM)]TJ -46.5746 -2.1118 TD [(5)-3578.3(2)0(1)-1491.2(F)-1161.5(100)-694(Cough,)-327.5(sputum)]TJ 12.7407 -1.0559 TD (\(18\))Tj 6.658 1.0559 TD [(+)-3680.7(+)-2428.7(?)-334.4(\(N\))-2880.6(+)-3712.3(7)0(2)]TJ /F5 1 Tf 19.8666 0 TD [(P)123.5(.)-331.7(aeruginosa)]TJ 0.0822 -1.0559 TD [(H.)-334.5(influenzae)]TJ /F4 1 Tf 7.6191 1.0559 TD [(L)85.5(VFX,)-335.3(EM)]TJ -46.9666 -2.1119 TD [(6)-3578.3(2)0(0)-1320.5(M)-1245.8(20)-947.4(Cough,)-327.5(sputum)]TJ 12.7407 -1.0559 TD (\(12\))Tj 6.658 1.0559 TD [(+)-3680.7(+)-2428.7(?)-334.4(\(N\))-2880.6(+)-3712.3(1)0(0)]TJ /F5 1 Tf 19.9488 0 TD [(H.)-334.5(influenzae)]TJ /F4 1 Tf 9.1682 0 TD (EM)Tj -48.5157 -2.1119 TD [(7)-3578.3(1)0(7)-1320.5(M)-1498.7(0)-1194.5(Cough,)-327.5(sputum)]TJ 12.9873 -1.0559 TD (\(2\))Tj 6.4114 1.0559 TD [(+)-3680.7(+)-2428.7(?)-334.4(\(N\))-2880.6(+)-3465.7(130)]TJ /F5 1 Tf 19.8666 0 TD [(P)123.5(.)-331.7(aeruginosa)]TJ /F4 1 Tf 7.7013 0 TD [(L)85.5(VFX,)-335.3(EM)]TJ -46.9666 -2.1118 TD [(8)-3578.3(4)0(7)-1491.2(F)-1661(0)-1194.5(Cough,)-327.5(sputum)]TJ 12.7407 -1.0559 TD (\(46\))Tj 6.658 1.0559 TD [(+)-3800.8(-)-2548.6(?)-334.4(\(N\))-2880.6(+)-3712.3(4)0(8)]TJ /F5 1 Tf 19.8666 0 TD [(P)123.5(.)-331.7(aeruginosa)]TJ 0.0822 -1.0559 TD [(H.)-334.5(influenzae)]TJ /F4 1 Tf 7.6191 1.0559 TD [(L)85.5(VFX,)-335.3(EM)]TJ -46.9666 -2.9971 TD [(F:)-467.8(female;)-471.2(M:)-463.6(male;)-471.5(SI:)-468.3(Brinckman)-466.5(smoking)-469.8(index;)-469.4(DOE:)-465.7(dyspnoea)-464.6(on)-466.9(exertion;)]TJ /F5 1 Tf 34.7444 0 TD [(P)123.5(.)-464.5(aeruginosa)]TJ /F4 1 Tf 5.6716 0 TD (:)Tj /F5 1 Tf 0.7398 0 TD [(Pseudomonas)-464.9(aeruginosa)]TJ /F4 1 Tf 10.4707 0 TD (;)Tj /F5 1 Tf 0.7398 0 TD (H.)Tj -52.3663 -1.0559 TD (influenzae)Tj /F4 1 Tf 4.072 0 TD (:)Tj /F5 1 Tf 0.803 0 TD [(Hemophilus)-538.3(influenzae)]TJ /F4 1 Tf 9.4085 0 TD [(;)-533(OFLX:)-533.3(ofloxacin;)-540(EM:)-529.8(erythromycin;)-541.3(L)85.5(VFX:)-536.6(levofloxacin;)-534.3(CAM:)-533.8(clarithromycin;)-544.8(+:)-533.7(with)]TJ -14.2835 -1.0559 TD [(complication;)-335.3(-:)-337.5(without)-335.7(complication;)-341.6(\(Y\):)-334.4(yes;)-330.1(\(N\):)-340.7(no;)-329.6(?:)-336.3(unknown.)]TJ ET 58.28 225.184 478.205 -0.51 re f 58.28 208.743 478.205 -0.51 re f 58.28 126.028 478.205 -0.51 re f BT /F3 1 Tf 8.966 0 0 8.966 58.28 229.493 Tm [(Table)-331.9(2.)-336.7(\261)-333.2(Chest)-330.7(radiography)-334.9(findings)]TJ /F4 1 Tf 0 -1.7072 TD [(Patient)-1222(Dextrocardia)-3038(Bronchiectasis)-3257.1(Centrilobular)-337.9(small)-340.2(nodules)-1125.3(Hyperinflation)-911.3(T)28.6(ramlines)-3545.1(Others)]TJ 0 -1.998 TD [(1)-5759.7(+)-3200.1(LML,)-331.5(LLL,)-334.3(RLing,)-333.4(RLL)-6548.1(-)-9181.3(+)-5242.4(+)-4325.6(Pneumonia)]TJ 0 -1.0559 TD [(2)-5759.7(+)-5956.9(LML,)-337.8(RLL)-9304.8(-)-9301.5(-)-5362.3(+)]TJ T* [(3)-5759.7(+)-3200.1(LML,)-331.5(LLL,)-334.3(RLing,)-333.4(RLL)-3803.9(+)-335.9(\(LLL,)-334.8(RLL\))-6434.7(+)-5356.2(-)-5393.9(Bullae)]TJ T* [(4)-5759.7(+)-4761.9(LML,)-331.5(LLL,)-334.3(RLL)-5365.7(+)-335.9(\(LLL,)-334.8(RLL\))-6554.8(-)-5476.1(-)]TJ T* [(5)-5759.7(+)-4426.8(LML,)-337.8(LLL,)-328(RLing)-5034.8(+)-335.9(\(LLL,)-334.8(RLL\))-6554.8(-)-5362.3(+)-2605.8(Atelectasis)-337.5(of)-335.1(LML)]TJ T* [(6)-5759.7(+)-7189.9(LML)-7789.6(+)-335.9(\(LLL,)-334.8(RLL\))-6554.8(-)-5362.3(+)-2605.8(Atelectasis)-337.5(of)-335.1(LML)]TJ T* [(7)-5759.7(+)-4540.6(LLL,)-328(RLing,)-333.4(RLL)-2248.5(+)-329.5(\(LML,)-338.3(LLL,)-328(RLing,)-339.7(RLL\))-3532.5(+)-5242.4(+)]TJ T* [(8)-5759.7(+)-3200.1(LML,)-331.5(LLL,)-334.3(RLing,)-333.4(RLL)-3803.9(+)-335.9(\(LLL,)-334.8(RLL\))-6434.7(+)-5242.4(+)-4325.6(Pneumonia)]TJ 0 -1.9411 TD 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[(ed)-149.9(vi)13.2(t)13.9(a)0(l)-152.3(c)0(a)14.7(p)0(a)20.8(c)0(i)18.5(t)0(y)-316.9(\()0(L)15.5(\))]TJ /F2 1 Tf 8.0635 0 TD (6)Tj /F4 1 Tf 0.9958 0 TD [(10)21.2(0\))-316.1(37)15.5(%,)-316.5(MM)17.3(F)-324.3(0)0(.)15.9(2)0(9)-314.5(L)]TJ /F9 1 Tf 9.7593 0.1992 TD (.)Tj /F4 1 Tf 0.2731 -0.1992 TD (s)Tj 7.472 0 0 6.641 503.263 468 Tm (-1)Tj 9.963 0 0 9.963 509.216 463.578 Tm [(\).)-315.7(Sp)16.3(u-)]TJ -20.0649 -1.0528 TD [(tu)13.2(m)-499(c)0(u)15.1(l)13.9(tu)13.2(re)-487.2(is)12(ol)18.9(at)18.4(ed)]TJ /F5 1 Tf 8.7179 0 TD [(P)137.4(.)-501.2(ae)15.1(ru)20(gi)18.9(no)15.5(sa)]TJ /F4 1 Tf 6.1173 0 TD -0.0138 Tc [(Ci)-13.8(li)-13.8(a)4.7(r)-13.8(y)-506.3(m)-13.8(o)4.3(r)-13.8(ph)-13.8(o)7.4(l)-13.8(og)-13.8(y)]TJ -14.8353 -1.0471 TD 0 Tc [(of)-441.3(th)18.8(e)-450.7(b)0(r)19.6(o)0(n)15.5(c)0(h)20.8(i)0(a)12.8(l)-447(ep)20.8(it)16.5(he)15.1(li)16.5(um)-437.2(re)13.5(ve)20.8(al)18.5(ed)-440.1(im)15.7(mo)18.1(ti)16.5(le)-442.5(ci)18.4(li)16.5(a)-445(a)0(n)15.1(d)]TJ 0 -1.0527 TD [(de)15.1(fe)19.2(ct)12.8(s)-462.9(o)0(f)-458.4(t)0(h)18.8(e)-467.8(dy)15.5(ne)20.8(in)-459.2(ar)19.2(ms)-461.1(\(f)18(ig)18.9(.)-467(1\).)-470.1(Chest)-479.1(radio)-8.2(graphy)]TJ 0 -1.0471 TD [(show)-8.2(ed)-406(dextrocardi)-11.9(a,)-405.6(reticular)-411.1(shadow)-10.1(s)-400.3(associa)-11.3(ted)-403.4(with)]TJ 0 -1.0527 TD [(tram)-10.6(lines)-169.5(and)-173.4(scattered)-175.4(fine)-172.5(nodula)-7.4(r)-167.4(densi)-7.8(ties)-174.4(in)-407.9(both)-415.2(lung)]TJ 0 -1.0471 TD [(fiel)-9.8(ds)-475(\(fig.)-475.6(2\).)-475.8(Chest)-479.1(CT)-442.9(images)-478.7(show)-8.2(ed)-474.2(dextrocardi)-11.9(a,)]TJ 0 -1.0015 TD [(bronchi)-9.7(ectas)-8.6(is)-534.3(and)-537.6(diffuse)-530.3(centr)-8.6(ilobular)-544.5(small)-536.8(nodule)-7.4(s)]TJ T* [(throu)-7.8(ghout)-478.5(both)-477.7(lungs)-479.7(\(fig.)-481.3(3\).)-475.8(The)-473.4(pati)-8.2(ent)-477.4(underwent)]TJ T* [(V)120.5(A)103.4(TS)-562.5(as)-560.8(a)-564.5(diagno)-7.4(stic)-561.4(procedu)-7.7(re.)-567.3(Microscopy)-573.2(at)-562(low)]TJ 0 -0.9958 TD [(magni)-9.7(fication)-288.8(of)-287.7(the)-283.9(lung)-284.3(speci)-8.2(men)-284.7(showed)-288.9(bronchioli)-11.1(tis)]TJ 0 -1.0015 TD [(in)-669.7(the)-665.2(centr)-8.6(ilobular)-669.7(lesi)-9.4(on)-661.6(associ)-10.2(ated)-666.3(wi)-7.8(th)-664(proxi)-7.8(mal)]TJ T* [(bronchi)-9.7(olect)-9.4(asis)-264.3(an)-7.6(d)-262.5(overi)-8.2(nflation)-271.3(with)-267.8(focal)-276.1(emphysema)]TJ 0 -0.9958 TD [(of)-515.3(the)-511.5(alveolar)-514.4(spaces)-514.6(\(fig)-8.6(.)-506.8(4a\).)-511.1(Higher)-519.3(magnific)-10.7(ation)]TJ 0 -1.0015 TD [(reveal)-9.8(ed)-388.9(that)-395.2(the)-386.3(wal)-9(ls)-386.4(of)-390.1(mem)-9(branous)-389.8(bronchi)-9.7(oli)-394(were)]TJ T* [(thic)-8.2(kened)-283.5(by)-286.1(fibrosis)-289.6(and)-287.2(infiltrati)-14.1(on)-280.4(of)-282(lym)-7.8(phocyt)-7.4(es)-282(and)]TJ T* [(plasm)-10.9(a)-399.5(cells)-403.2(associated)-409(with)-404.4(or)-401.5(without)-403.4(perib)-8.2(ronchiolar)]TJ ET 1 i 58.28 768.302 478.205 -0.51 re f 58.28 742.393 478.205 -0.51 re f 58.28 640.743 478.205 -0.454 re f BT /F3 1 Tf 8.966 0 0 8.966 58.28 772.667 Tm [(Table)-331.9(3.)-336.7(\261)-333.2(Pulmonary)-331.8(function)-337.2(tests)]TJ /F4 1 Tf 0 -1.7135 TD [(Patient)-3833.4(FVC)]TJ 6.658 -1.0496 TD 0.3318 Tc (L%)Tj 5.2923 1.0496 TD 0 Tc (FEV)Tj 7.173 0 0 7.173 182.211 757.304 Tm (1)Tj 8.966 0 0 8.966 172.913 747.893 Tm (L)Tj 3.5092 1.0496 TD (FEV)Tj 7.173 0 0 7.173 221.159 757.304 Tm (1)Tj 8.966 0 0 8.966 224.787 757.304 Tm (/FVC)Tj -0.4489 -1.0496 TD (%)Tj 4.1289 1.0496 TD [(R)71.6(V/TLC)]TJ 1.3215 -1.0496 TD (%)Tj /F11 1 Tf 4.0909 1.0496 TD (D)Tj /F4 1 Tf 0.6639 0 TD (N)Tj 6.725 0 0 5.977 318.727 755.83 Tm (2)Tj 8.966 0 0 8.966 299.225 747.893 Tm (%)Tj 5.3998 1.0496 TD (MMF)Tj 0.0569 -1.0496 TD (L)Tj /F9 1 Tf 0.607 0.2213 TD (.)Tj /F4 1 Tf 0.2719 -0.2213 TD (s)Tj 6.725 0 0 5.977 359.49 751.861 Tm (-1)Tj /F5 1 Tf 8.966 0 0 8.966 386.816 757.304 Tm (D)Tj /F4 1 Tf 7.173 0 0 7.173 393.279 757.304 Tm (L,CO)Tj 8.966 0 0 8.966 412.327 757.304 Tm (mL)Tj /F9 1 Tf 1.3784 0.2276 TD (.)Tj /F4 1 Tf 0.2656 -0.2276 TD (min)Tj 6.725 0 0 5.977 440.901 761.329 Tm (-1)Tj /F9 1 Tf 8.966 0 0 8.966 446.457 759.345 Tm (.)Tj /F4 1 Tf -5.4567 -1.2772 TD (mmHg)Tj 6.725 0 0 5.977 422.249 751.861 Tm (-1)Tj 8.966 0 0 8.966 430.809 747.893 Tm (%)Tj /F5 1 Tf 3.9202 1.0496 TD (P)Tj /F4 1 Tf 7.173 0 0 7.173 471.345 757.304 Tm (a,O)Tj 6.725 0 0 5.977 481.436 755.83 Tm (2)Tj 8.966 0 0 8.966 464.485 747.893 Tm (mmHg)Tj /F5 1 Tf 4.4576 1.0496 TD (P)Tj /F4 1 Tf 7.173 0 0 7.173 509.896 757.304 Tm (a,CO)Tj 6.725 0 0 5.977 524.749 755.83 Tm (2)Tj 8.966 0 0 8.966 505.417 747.893 Tm (mmHg)Tj -49.8688 -2.0044 TD [(1)-5171.6(2.09)-330.2(\(76\))-2813.6(1.27)-4073.3(61)-4450.3(44)-3350.1(16.3)-2979.5(0.78)]TJ 6.276 0 0 6.276 413.348 729.921 Tm 0.0001 Tc (ND)Tj 8.966 0 0 8.966 470.891 729.921 Tm 0 Tc [(77)-3729.5(41)]TJ -46.0181 -1.0559 TD [(2)-5171.6(3.33)-330.2(\(84\))-2813.6(2.16)-4073.3(65)-4450.3(48)-3603.1(2.5)-3473.2(1.1)-3928.4(31.2)-336.5(\(139\))-3799.5(81)-3729.5(37)]TJ T* [(3)-5171.6(1.47)-330.2(\(56\))-2813.6(0.71)-4073.3(48)-4450.3(64)-3603.1(8.4)-3226.6(0.27)-3927.9(14.0)-330.2(\(81\))-4052.9(71)-3729.5(37)]TJ T* [(4)-5171.6(2.08)-330.2(\(66\))-2813.6(1.09)-4073.3(52)-4450.3(59)-3603.1(3.5)-3226.6(0.48)]TJ 6.276 0 0 6.276 413.348 701.518 Tm 0.0001 Tc (ND)Tj 8.966 0 0 8.966 470.891 701.518 Tm 0 Tc [(71)-3729.5(46)]TJ -46.0181 -1.0559 TD [(5)-5171.6(2.81)-330.2(\(87\))-2813.6(1.69)-4073.3(60)-4450.3(33)-3603.1(3.5)-3852.6(1)-4318.1(23.2)-330.2(\(1)31.7(18\))-3818.5(84)-3729.5(37)]TJ 0 -1.0496 TD [(6)-5171.6(4.36)-330.2(\(90\))-2813.6(3.25)-4073.3(74)-4450.3(29)-3603.1(1.9)-3226.6(2.53)-3675(37.7)-336.5(\(127\))-3799.5(80)-3729.5(42)]TJ 0 -1.0559 TD [(7)-5171.6(2.78)-330.2(\(63\))-2813.6(1.03)-4073.3(37)-4450.3(33)-3350.1(18.5)-2979.5(0.29)-3675(28.4)-336.5(\(100\))-3799.5(86)-3729.5(37)]TJ T* 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Tf 8.3968 0 TD (D)Tj /F4 1 Tf 7.173 0 0 7.173 139.975 617.839 Tm (L,CO)Tj 8.966 0 0 8.966 156.076 617.839 Tm [(:)-356(carbon)-351.5(monoxide)-360.4(diff)10.4(using)-355.1(capacity)-353.9(of)-360.4(the)-354.7(lung;)]TJ /F5 1 Tf 20.7075 0 TD (P)Tj /F4 1 Tf 7.173 0 0 7.173 347.131 617.839 Tm (a,O)Tj 6.725 0 0 5.977 357.222 616.365 Tm (2)Tj 8.966 0 0 8.966 360.624 617.839 Tm [(:)-349.6(arterial)-364.7(oxygen)-350.8(tension;)]TJ /F5 1 Tf 10.5276 0 TD (P)Tj /F4 1 Tf 7.173 0 0 7.173 460.46 617.839 Tm (a,CO)Tj 6.725 0 0 5.977 475.313 616.365 Tm (2)Tj 8.966 0 0 8.966 478.658 617.839 Tm [(:)-356(arterial)-358.4(carbon)]TJ -46.8844 -1.0559 TD [(dioxide)-336.1(tension;)]TJ 6.276 0 0 6.276 119.055 608.371 Tm 0.0001 Tc (ND)Tj 8.966 0 0 8.966 128.069 608.371 Tm 0 Tc [(:)-337(not)-329.7(determined.)-339.8(\(1)-335.1(mmHg)]TJ /F10 1 Tf 11.1536 0 TD (=)Tj /F4 1 Tf 0.5501 0 TD [(0.133)-336(kPa.\))]TJ ET 58.28 277.398 478.205 -0.51 re f 91.389 262.431 91.616 -0.284 re f 185.896 262.431 166.507 -0.284 re f 58.28 236.523 478.205 -0.454 re f 58.28 163.332 478.205 -0.51 re f BT /F3 1 Tf 8.966 0 0 8.966 58.28 281.764 Tm [(Table)-331.9(4.)-336.7(\261)-333.2(Pathological)-334.3(findings)]TJ /F4 1 Tf 4.015 -1.7072 TD [(Lesions)-339.6(of)-335.1(bronchiolitis)-4686.2(Histopathological)-338.2(features)]TJ -4.015 -1.6692 TD [(Patient)-1342.2(RB)-1152.9(MB)-1155.2(Infiltrating)]TJ 10.692 -1.0559 TD (cell)Tj 3.857 1.0559 TD (Bronchio-)Tj 0.5627 -1.0559 TD (lectasis)Tj 4.5019 1.0559 TD (Pneu-)Tj -0.0885 -1.0559 TD (monia)Tj 3.4397 1.0559 TD [(LH)-954.2(OB)-955.4(Emphysema)]TJ 11.4951 -1.0559 TD [(Pathological)-336.4(diagnosis)]TJ 11.2295 1.0559 TD [(Sampling)-329.7(method)]TJ -0.019 -1.0559 TD [(\(segment)-337(of)-335.1(lobe\))]TJ -45.6704 -1.998 TD [(3)-3964(+)-1752.2(++)-1980.5(N,)-328.2(L,)-334.7(P)-3077.4(+)0(+)-3080.7(+)0(+)-2138.6(-)-1985.9(-)-1878.4(+)-329.5(\(Bullae\))-1606.6(Membranous)-334.3(bronchiolitis)]TJ 34.0046 -1.0559 TD [(Respiratory)-335.3(bronchiolitis)]TJ 13.55 1.0559 TD (Autopsy)Tj -47.5546 -2.1119 TD [(7)-3964(+)-1467.7(+++)-1703(N,)-328.2(L,)-334.7(P)-3077.4(+)0(+)-3485.4(-)-2415.8(+)-1745.9(+)-1543.5(+)-335.9(\(FE,)-333.2(CE\))-1386(Membranous)-334.3(bronchiolitis)]TJ 38.2852 -1.0559 TD (OB)Tj 7.1828 1.0559 TD [(V)123.6(A)104.7(TS)-336.2(\(Rt.)-331.9(S8,)-335.6(S9\))]TJ -45.4681 -2.1118 TD [(8)-3964(+)-1467.7(+++)-1184.6(N,)-334.5(L,)-334.7(P)103.1(,)-331.7(F)-2843.4(+)-3762.9(-)-2131.3(+)0(+)-1468.4(+)-2473(+)-329.5(\(FE\))-2063.2(Membranous)-334.3(bronchioloitis)]TJ 38.2852 -1.0559 TD (OB)Tj -4.2806 -1.0559 TD [(Respiratory)-335.3(bronchiolitis)]TJ 11.4951 2.1119 TD [(V)123.6(A)104.7(TS)-336.2(\(Lt.)-330.7(S6,)-335.6(S8\))]TJ -45.4997 -4.0593 TD [(The)-387.4(intensity)-391.6(of)-392(the)-386.3(histopathological)-391.8(features)-392.8(is)-388.3(graded)-389.5(on)-391(a)-385(semiquantitative)-400.3(scale)-386.1(of)-392(-)-386.2(\(none\))-390.7(to)-387.1(+++)-394.2(\(intense\).)-391.4(RB:)-389.7(respiratory)]TJ 0 -1.0496 TD 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7.472 0 0 7.472 265.833 797.499 Tm 0.0001 Tc [(S.)-336(HOMMA)-339.8(ET)-256.2(AL.)]TJ ET endstream endobj 21 0 obj << /ProcSet [/PDF /Text ] /Font << /F2 5 0 R /F3 6 0 R /F4 7 0 R /F5 8 0 R /F9 12 0 R /F10 18 0 R /F11 22 0 R >> /ExtGState << /GS2 13 0 R >> >> endobj 23 0 obj << /Type /XObject /Subtype /Image /Name /Im1 /Width 230 /Height 203 /BitsPerComponent 8 /ColorSpace /DeviceGray /Length 16580 /Filter /DCTDecode >> stream AdobedC    o!1AQ"aq2 #BR3$bC4% rS&cD5Ts6'E7F򃓣dU()8GHVe*9:IJWXYZftugvwhijxyz?1m;o ծ%Ji)?ptk CJj.0ͲEr{qY "h*`NšDaq;Iq➿dBGXUy?xt˱=Q+-ķCTKHM6U *ҰdbGojl:s'v!rVxX}?jTnU[v7ԋ|ޡq\R rGtU_Zi~ ]IzJ!fltxw1R11 E!r=96: 'Y㤰(]@{(PIX=9b+N&'%M.)^BĀ@%ֿR9S)3U("[ h]E*#,4Qϓ j%F6x\=g݄jh ׊#IdNǶ?:~G3=e4xmB0DzK;iueZƩue ӈ_T^c yJ/UCNt).Y0ؼ-[qK@n^t;D/4>zrTR19Tr<@lA0d&K46K+>:qSzX&I/~"HaiQ_F;^ E|$XElI= ċV`\w@$2,J-l6i+]MdiH]O85M|`Z(bڋ (iۋrL򜘦-4xU9b#D&aPNwӮb\Rbj8$#r82/[WKQɗtL:$Qm1fsǬcpi)O2<@F1Ow]Oi`f(I4U_p{o,g\ʕ Pea䝡%EhnYLf$º8:>74hqǍi8I vy>K8${]:O 3jUV2n,7B}"s%qwLXGSzz8K]IjTCz3̯W 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[(showe)-9.3(d)-273.9(O)0(B)-283.3(where)-283.3(the)-278.2(lum)-7.8(ina)-278.2(of)-282(membranou)-9.9(s)-280.8(bronchioli)]TJ T* [(were)-339.4(obliterat)-13.1(ed)-332(by)-337.3(fibrous)-342.2(scars)-338.7(\(figs.)-341(5a)-332(and)-338.4(b\).)]TJ 1.0015 -1.0471 TD [(Th)17.1(e)-200.3(s)0(c)19.6(h)0(e)15.1(m)0(a)17.7(t)0(i)16.5(c)-200.3(re)19.2(co)15.1(ns)20(tr)17.3(uc)15.1(ti)22.2(on)-195(of)-185.2(th)13.2(e)-200.3(s)0(e)19.6(c)0(t)18.4(i)0(o)18.9(n)0(s)-190.5(f)0(o)13.9(c)0(u)20.8(s)0(i)17.7(n)0(g)-189.3(o)0(n)]TJ -1.0015 -1.0755 TD [(th)18.9(e)-211.7(c)0(e)14.7(n)0(t)18.9(r)0(i)17.3(l)0(o)18.9(b)0(u)15.5(l)0(a)18.4(r)-212.9(le)18.4(si)17.7(on)21.2(s)-212.5(s)0(h)14.4(o)0(w)17.3(e)0(d)-201.1(m)0(e)17.7(m)0(b)18.1(r)0(a)13.5(n)0(o)21.2(u)0(s)-201.9(b)0(r)14(o)0(n)21.2(c)0(h)15.1(i)0(o)18.9(l)0(i)16.5(t)0(i)16.5(s)]TJ T* [(as)19.6(so)14.3(ci)18.4(at)18.4(ed)-497(wi)20.6(th)-499(pe)20.8(ri)17.3(br)14(on)21.2(ch)15.1(io)18.9(la)18.4(r)-503.1(f)0(i)17.3(b)0(r)13.9(o)0(s)20(i)0(s)17.7(,)-501.2(fi)11.6(br)19.6(o-)19.6(hy)15.5(al)18.4(in)18.9(ou)15.5(s)]TJ T* [(sc)19.6(ar)13.5(s,)-235.7(l)13.9(y)0(m)12.4(p)0(h)21.2(o)0(i)13.2(d)-239.8(hy)15.5(pe)20.8(rp)13.9(la)18.4(si)17.7(a)-245.9(a)0(n)20.8(d)-245.5(in)18.9(fi)17.3(lt)16.5(ra)19.2(ti)16.5(on)-234.8(of)-236.4(ne)15.1(ut)18.9(ro)19.6(ph)15.5(il)16.5(s,)]TJ T* [(ly)18.9(mp)18.1(ho)15.5(cy)15.1(te)18.4(s)-258(a)0(n)20.8(d)-256.8(pl)18.9(as)13.9(ma)-249.8(ce)20.4(ll)16.5(s.)-247(Th)17.1(e)-257.2(a)0(l)12.8(v)0(e)20.8(o)0(l)18.9(a)0(r)-248.2(s)0(p)14.4(a)0(c)20.4(e)0(s)14(,)-256.5(al)18.4(ve)15.1(o-)]TJ T* [(la)18.4(r)-201.5(d)0(u)15.5(c)0(t)18.4(s)-201.1(\(A)15.7(D\))-194.8(an)15.1(d)-199.9(r)0(e)19.2(s)0(p)14.4(i)0(r)17.3(a)0(t)18.4(o)0(r)19.6(y)-205.6(br)19.6(on)21.2(ch)15.1(io)18.9(li)-194.1(\(R)14.9(B)11.6(\))-207.2(w)12.4(e)0(r)13.5(e)-200.3(di)18.9(la)18.4(te)12.8(d)]TJ T* [(in)-208.8(as)19.6(so)20(ci)12.8(at)18.5(io)18.9(n)-217(w)0(i)20.6(t)0(h)-208.8(f)0(o)19.6(c)0(a)14.7(l)-213.7(em)12(ph)21.2(ys)14.4(em)17.7(a)-217.4(\()0(f)18(i)0(g)18.9(.)-216.6(6\).)-214.1(Acco)-7.8(rding)-229.7(to)]TJ T* [(these)-406.5(pathol)-9.7(ogical)-408.5(findings,)-412.4(this)-407.3(case)-403.8(was)-406.2(diagno)-7.4(sed)-407.9(as)]TJ T* [(having)-456.9(membranou)-9.9(s)-451.5(bronchioli)-11.1(tis,)-452.5(OB)-448.3(and)-452.3(perib)-8.2(ronch-)]TJ T* [(iolar)-352(lym)-7.8(phoid)-353.3(hyperplasi)-10.3(a)-348.3(with)-353.2(focal)-355.7(emphysema)-357(asso-)]TJ T* [(ciated)-340.6(with)-336.1(KS.)]TJ /F5 1 Tf 25.1977 16.9465 TD [(Pat)-8.8(ient)-235.8(8.)]TJ /F4 1 Tf 4.0858 0 TD [(A)-226.6(4)0(7)15.5(-)0(y)19.6(r)20.4(-o)13.9(ld)-214.5(fe)13.5(ma)17.7(le)-220.6(pr)19.6(es)19.6(en)15.1(te)18.4(d)-228.4(w)0(i)14.9(t)13.9(h)-228.4(a)-228.8(1)-228.4(y)0(r)-213.7(h)0(i)13.2(s)0(t)17.7(o)0(r)19.6(y)]TJ -4.0858 -1.0698 TD [(of)-236.4(co)15.1(ug)21.2(h)-245.5(a)0(n)20.8(d)-245.5(sp)20(ut)13.2(um)18.1(.)-239.4(S)0(h)16.3(e)-245.9(ha)20.8(d)-245.5(a)-240.2(hi)13.2(st)17.7(or)19.6(y)-245.5(o)0(f)-230.7(c)0(h)15.1(r)0(o)19.6(n)0(i)18.9(c)-245.9(pa)15.1(ns)20(in)18.8(-)]TJ 0 -1.0755 TD [(us)14.4(it)16.5(is)17.7(.)-193.9(L)0(u)17.1(n)0(g)-189.3(a)0(u)15.1(s)0(c)19.6(u)0(l)13.2(t)0(a)18.4(t)0(i)16.5(o)0(n)-189.3(r)0(e)19.2(v)0(e)15.1(a)0(l)18.5(e)0(d)-189.7(c)0(o)15.1(a)0(r)19.2(s)0(e)-190.9(c)0(r)19.2(a)0(c)14.7(k)0(l)18.9(e)0(s)-190.9(o)0(n)-189.3(t)0(h)18.9(e)-200.3(bi)18.8(-)]TJ 0 -1.0698 TD [(la)12.8(te)18.4(ra)19.2(l)-225.1(l)0(o)18.8(w)0(e)16.9(r)-224.3(lu)18.9(ng)-212.1(fi)17.3(el)12.8(ds)20(.)-222.3(P)11.4(ul)13.2(mo)18.1(na)20.8(ry)-219.4(fu)19.6(nc)20.8(ti)16.5(on)-217.8(te)18.4(st)17.7(s)-223.9(r)0(e)19.2(v)0(e)15.1(a)0(l)18.4(e)0(d)]TJ 0 -1.0755 TD [(ob)15.5(st)17.7(ru)19.6(ct)12.8(iv)18.8(e)-183.3(i)0(m)15.7(p)0(a)15.1(i)0(r)17.3(m)0(e)17.7(n)0(t)-180.3(w)12.4(it)16.5(h)-188.6(s)0(l)17.7(i)0(g)18.9(h)0(t)-174.6(h)0(y)15.5(p)0(o)15.5(x)0(a)20.8(e)0(m)17.7(i)0(a)-180.7(\()0(F)20.4(E)0(V)]TJ 7.97 0 0 7.97 513.808 493.228 Tm 0 Tw (1)Tj 9.963 0 0 9.963 519.307 493.228 Tm [(1.)15.9(06)]TJ -21.0778 -1.0698 TD [(L,)-232.9(F)11.4(E)0(V)]TJ 7.97 0 0 7.97 338.57 482.57 Tm (1)Tj 9.963 0 0 9.963 344.92 482.57 Tm [(59)21.2(%,)-231.1(MM)17.3(F)-239(0)0(.)15.9(9)0(3)-229.2(L)]TJ /F9 1 Tf 7.3806 0.1992 TD (.)Tj /F4 1 Tf 0.2731 -0.1992 TD (s)Tj 7.472 0 0 6.641 424.913 486.992 Tm (-1)Tj 9.963 0 0 9.963 430.866 482.57 Tm -0.018 Tc [(,)-257.4(a)-18(rt)-18(er)-18(i)-6.4(a)-18(l)-244.2(o)-18(xy)-18(ge)-18(n)-247.6(t)-18(en)-18(si)-18(on)-257.8(1)-18(0)]TJ -12.2005 -1.0698 TD 0 Tc [(kP)16.3(a)-393.8(\()0(7)19.6(5)-387.7(mm)14.9(Hg)17.3(\)\))18(.)-393(S)11.4(pu)15.5(tu)18.9(m)-390.9(c)0(u)15.1(l)0(t)16.5(u)0(r)19.6(e)-388.1(is)17.7(ol)13.2(at)18.5(ed)]TJ /F5 1 Tf 17.4586 0 TD [(H.)-386.3(i)13.9(n)0(f)13.2(l)0(u)18.9(e)0(n)20.8(z)0(a)14.3(e)]TJ /F4 1 Tf -17.4586 -1.0755 TD [(an)15.1(d)]TJ /F5 1 Tf 1.8494 0 TD [(P)131.7(.)-427.2(ae)20.8(ru)14.4(gi)18.9(no)15.5(sa)]TJ /F4 1 Tf 5.5369 0 TD [(.)-427.2(M)0(o)13.6(r)0(p)19.6(h)0(o)15.5(l)13.9(og)15.5(ic)18.4(al)-419.7(an)15.1(al)18.4(ys)14.4(i)13.9(s)-428.7(of)-424.2(th)18.9(e)-428(b)0(r)13.9(o)0(n)21.2(-)]TJ -7.3863 -1.0698 TD [(ch)15.1(ia)18.4(l)-156.8(e)0(p)15.1(i)0(t)16.5(h)0(e)20.8(l)0(i)16.5(u)0(m)-152.6(r)0(e)19.2(v)0(e)15.1(a)0(l)18.5(e)0(d)-149.9(i)0(m)15.7(m)0(o)18.1(t)0(i)16.5(l)0(e)-334.4(c)0(i)18.5(l)0(i)16.5(a)-342.6(an)15.1(d)-342.2(d)0(e)20.8(f)0(e)19.2(c)0(t)12.8(s)-343.4(of)-333.2(th)18.9(e)]TJ T* [(ci)12.8(li)22.2(ar)13.5(y)-473.1(d)0(y)21.2(n)0(e)15.1(i)0(n)-459.2(a)0(r)13.5(m)0(s)16.9(.)-472.7(C)11.6(h)0(e)15.1(s)0(t)-460.3(r)0(a)13.5(d)0(i)18.9(o)0(g)15.5(r)0(a)19.2(p)0(h)15.5(y)-467.4(sh)14.3(ow)17.3(ed)-462.9(de)20.8(xt)13.2(ro)19.6(-)]TJ 0 -1.0755 TD [(ca)14.7(rd)19.6(ia)12.8(,)-324.7(r)0(e)13.5(t)0(i)22.2(c)0(u)15.1(l)0(a)18.5(r)-332.4(sh)20(ad)15.1(ow)17.3(s)-326.3(a)0(s)14(s)0(o)20(c)0(i)18.4(a)0(t)18.5(e)0(d)-320.6(w)0(i)14.9(t)0(h)-322.6(t)0(r)17.3(a)0(m)17.7(l)0(i)16.5(n)0(e)20.8(s)0(,)-321(b)0(r)13.9(o)0(n)21.2(-)]TJ 0 -1.0698 TD [(ch)15.1(ie)18.4(ct)18.5(as)13.9(is)-147.4(an)15.1(d)-154.4(s)0(c)14(a)0(t)18.4(t)0(e)18.5(r)0(e)19.2(d)-160.1(fi)17.3(ne)-314.9(no)15.5(du)21.2(la)12.8(r)-321(d)0(e)15.1(n)0(s)20(i)0(t)16.5(i)0(e)18.4(s)-326.3(in)-311.2(bo)15.5(th)-316.9(lu)18.9(ng)]TJ T* [(fi)17.3(el)12.8(ds)20(.)-472.7(C)0(h)16.5(e)0(s)19.6(t)-475.5(CT)-437.2(im)15.7(ag)20.8(es)-464.1(sh)14.4(ow)17.3(ed)-462.9(de)15.1(xt)18.9(ro)19.6(ca)14.7(rd)19.6(ia)18.4(,)-478.4(b)0(r)19.6(o)0(n)21.2(c)0(h)15.1(i)0(-)]TJ 0 -1.0755 TD [(ec)14.7(ta)18.4(si)17.7(s)-451.5(a)0(n)15.1(d)-450.3(di)13.2(f)20.4(f)0(u)19.6(s)0(e)-447(c)0(e)20.4(n)0(t)18.9(r)0(i)17.3(l)0(o)13.2(b)0(u)21.2(l)0(a)18.4(r)-457.6(sm)16.9(al)18.5(l)-452.7(n)0(o)15.5(d)0(u)21.2(l)0(e)18.5(s)-457.2(t)13.9(h)0(r)13.9(o)0(u)21.2(g)0(h)15.5(-)]TJ 0 -1.0698 TD [(ou)15.5(t)-333.2(b)0(o)15.5(t)13.9(h)-336.5(l)0(u)18.9(n)0(g)15.5(s)-332(\(f)18(ig)18.9(.)-336.1(7\).)-333.6(The)-342.6(pati)-8.2(ent)-346.5(underwent)-351.3(V)126.2(A)97.7(TS)-340.6(for)]TJ T* [(eva)-8.8(luation)-388.5(of)-384.4(histopat)-9.1(hological)-390.4(featu)-8.6(res)-386.8(of)-384.4(these)-383.8(diffuse)]TJ 0 -1.0755 TD [(cen)-8.8(trilobular)-521.5(lesions.)-519.7(Micr)-9.4(oscopy)-518.3(at)-516.5(a)-513.3(low)-515.1(magnific)-10.7(a-)]TJ 0 -1.0698 TD [(tion)-514.3(of)-509.6(the)-511.5(lung)-511.9(show)-8.2(ed)-508.4(bronchi)-9.7(olitis)-516.1(in)-510.4(the)-511.5(centr)-8.6(ilo-)]TJ 0 -1.0755 TD [(bular)-389.5(lesion)-386.5(and)-384(overi)-8.2(nflated)-388.1(alveol)-10.1(ar)-384.8(spaces)-383.8(wi)-7.8(th)-379.5(focal)]TJ 0 -1.0698 TD [(emphy)-7.4(sema)-8.2(.)-165.4(H)0(i)-7.8(gher)-170.1(magnific)-10.7(ation)-174(revealed)-176.7(that)-378.1(the)-375(walls)]TJ T* [(of)-503.9(membranou)-9.9(s)-497(bronchi)-9.7(oli)-502.1(were)-498.8(thic)-8.2(kened)-499.7(by)-502.3(infiltra-)]TJ 0 -1.0755 TD [(tion)-446(of)-435.6(lymp)-8.6(hocytes)-442.2(and)-440.9(plasma)-444.6(cells)-443.1(accompa)-10.1(nied)-438.3(by)]TJ 0 -1.0698 TD 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P&&e LId*8bMf%MOLOᱼY^TʒsGdf:We~MtZqpMV…>}I/<(G"GI6Iqa)XύA%Q)kLS6׌lcej4xqp12e+SV@(fyc{MV=TrV i*+1/Q+N(+zx)[kUފ#c50T؎|˯UMB~4Lj9&@Xo{/oUȰf u.Q2O O_u? ;VTZ86}9TAEXC^T؎ FK?)2)pU@ P<)="a]@ɴ*5Z -JRTcMHbȾՓ]|$+VSҭMD&e*h)9|RFѣiV%x +6z:b[?# z #dzJ(hjcdq%yQRK`bao`i+W2UFY#y1*"?3=H7"K!`9:/#ͅɃ8>ħZ+i]NQXKrS̹*:sU3idUitbY*m> stream BT /F7 1 Tf 9.963 0 0 9.963 149.613 347.074 Tm 0 g /GS2 gs 0 Tc [(Discuss)-9.1(ion)]TJ /F4 1 Tf -8.1659 -2.0998 TD [(In)-367.3(19)15.5(33)21.2(,)-381.7(K)]TJ 6.974 0 0 6.974 112.989 326.154 Tm 0.0001 Tc [(AR)67.2(T)83.8(AGE)24.1(NER)]TJ 9.963 0 0 9.963 157.436 326.154 Tm 0 Tc [([1)19.6(])-389.3(described)-394.5(a)-388.1(syndro)-7.4(me)-392(char-)]TJ -9.9528 -1.0755 TD [(acter)-9(ized)-216.8(by)-212.1(the)-215.6(tri)-8.6(ad)-212.5(of)]TJ /F5 1 Tf 9.4691 0 TD [(situs)-215.8(in)-214.5(versus)]TJ /F4 1 Tf 5.5483 0 TD [(,)-210.9(bronchi)-9.7(ectas)-8.6(is)-215.7(and)]TJ -15.0174 -1.0698 TD [(chroni)-9(c)-262.9(pansi)-7.8(nusitis)-9.2(.)-267.8(The)-268.6(disorder)-275(is)-266.9(inher)-8.2(ited)-270(as)-264.9(an)-269.4(auto-)]TJ 0 -1.0755 TD [(soma)-7.8(l)-526.7(recess)-9.8(ive)-528.6(trait.)-536.9(Males)-533.7(and)-531.9(females)-532.7(are)-533.9(affected)]TJ T* [(equall)-10.1(y)61.8(.)-330.4(Recentl)-10.3(y)61.8(,)-330.4(the)-335.1(syndro)-7.4(me)-329.4(has)-333.9(be)-7.6(en)-332(classified)-344.3(as)-333.2(a)]TJ 0 -1.0698 TD [(PCD.)-312.1(Diagnosi)-10.7(s)-309.2(o)0(f)-304.7(PCD)-311.8(is)-306.7(dep)-8.4(endent)-309.4(on)-308.8(the)-312.4(demonstra)-10.3(-)]TJ 0 -1.0755 TD [(tion)-184.2(of)-185.2(abnorm)-9.7(al)-180.7(ciliary)-191.3(mot)-7.8(ility)-184.1(and)-184.8(ultr)-9.4(astructur)-11.1(al)-180.7(defect)-9.8(s)]TJ 0 -1.0698 TD [(of)-236.4(the)-232.7(cilia)-239.4([4,)-236.8(5].)-231.1(In)-236.4(1990,)-236.7(A)]TJ 6.974 0 0 6.974 170.816 251.32 Tm 0.0001 Tc [(MIT)63.4(ANI)]TJ /F5 1 Tf 9.963 0 0 9.963 197.575 251.32 Tm 0 Tc [(et)-237.6(al.)]TJ /F4 1 Tf 2.1966 0 TD [([7])-238.8(reported)-240.1(nine)]TJ -16.1782 -1.0755 TD [(cases)-189.5(of)-185.2(PCD,)-186.9(including)-190.8(six)-182.3(cases)-189.5(of)-185.2(KS,)-187.1(two)-185(cases)-189.5(of)-185.2(DPB)]TJ T* [(and)-418.1(one)-418.1(case)-415.2(of)-418.5(bronchi)-9.7(ectasis.)-423.8(They)-417.3(described)-423(diffuse)]TJ 0 -1.0698 TD [(micronodul)-11.8(ar)-253.9(shadows)-256.7(on)-251.9(the)-249.8(chest)-252.9(radio)-8.2(graph)-256.2(in)-248.6(one)-253.1(out)]TJ 0 -1.0755 TD [(of)-373(six)-370.1(patients)-379.4(with)-370.2(KS)-374.6(and)-366.9(in)-373.8(both)-369.6(pati)-8.2(ents)-371.2(with)-375.9(DPB.)]TJ 0 -1.0698 TD [(However)18.5(,)-222.3(their)-226.8(report)-226.8(lacked)-230.1(hist)-9(opathologi)-9.5(cal)-227.4(analysis)-230.3(of)]TJ 0 -1.0755 TD [(diffuse)-331.2(micronodu)-14.4(lar)-336.7(lesions)-337.2(in)-339.7(these)-338.2(cases.)]TJ 1.0015 -1.0528 TD [(DP)18.1(B)-210.3(h)0(a)20.8(s)-206.8(be)20.8(en)-201.1(no)21.2(te)18.4(d)-205.6(i)0(n)-197.4(J)0(a)13.9(p)0(a)20.8(n)-205.6(si)17.7(nc)15.1(e)-206(1)0(9)21.2(6)0(9)-195(a)0(s)-196.6(a)-206(ne)15.1(w)-203.9(c)0(l)18.5(i)0(n)13.2(i)0(c)18.4(-)]TJ -1.0015 -1.0698 TD [(op)15.5(at)18.4(ho)21.2(lo)13.2(gi)18.9(c)-348.3(e)0(n)20.8(t)0(i)16.5(t)0(y)81.4(,)-347.5(ch)20.8(ar)13.5(ac)20.4(te)12.8(ri)17.3(ze)20.4(d)-347.9(b)0(y)-337.3(r)0(e)19.2(s)0(p)14.4(i)0(r)17.3(a)0(t)18.4(o)0(r)19.6(y)-347.9(br)19.6(on)15.5(ch)15.1(io)18.9(-)]TJ 0 -1.0755 TD [(li)16.5(ti)16.5(s)-246.7(a)0(n)15.1(d)-251.2(pe)15.1(ri)17.3(br)19.6(on)21.2(ch)15.1(io)18.9(li)16.5(ti)16.5(s)-252.3(w)0(h)17.3(i)0(c)18.4(h)-251.2(ar)19.2(e)-251.6(d)0(i)18.9(f)14.7(fu)19.6(se)19.6(ly)-242.9(di)18.9(ss)13.2(em)17.7(in)18.9(at)18.4(ed)]TJ 0 -1.0698 TD [(th)18.9(ro)13.9(ug)21.2(ho)15.5(ut)-430.7(th)13.2(e)-439.3(l)0(u)13.2(n)0(g)21.2(s)-445.8(bi)18.9(la)18.4(te)18.4(ra)13.5(ll)16.5(y)73.2(,)-444.2(es)19.6(pe)15.1(ci)18.4(al)18.5(ly)-436.4(in)-436.4(t)13.9(h)0(e)-440.1(l)13.9(ow)11.6(er)]TJ 0 -1.0755 TD [(lo)18.9(be)15.1(s,)-252.7(an)20.8(d)-262.5(d)0(i)18.9(f)14.7(fu)19.6(se)-253.5(ce)20.4(nt)13.2(ri)17.3(lo)18.9(bu)21.2(la)12.8(r)-258.4(s)0(m)16.9(a)0(l)12.8(l)-259.2(no)15.5(du)21.2(le)18.4(s)-263.7(o)0(n)-251.9(c)0(h)15.1(e)0(s)19.6(t)-264.9(C)11.6(T)]TJ T* [([6)19.6(,)-427.2(1)27.7(1].)-424.6(Fu)-6.4(rthermor)-11.1(e,)-422.7(seconda)-7.7(ry)-429.9(bronchi)-9.7(olectasis)-433(in)-430.7(the)]TJ 0 -1.0698 TD [(middle)-297.4(lobe)-290.4(and/or)-293.5(ling)-7.8(ula)-289.6(is)-289.6(freque)-8.6(ntly)-292.3(observ)-7.8(ed)-292.2(in)-288.4(pro-)]TJ 25.1977 25.6871 TD [(gress)-8.2(ive)-312.4(DPB)-317.4([12].)-313.9(Al)-7.8(though)-314.2(the)-312.4(aeti)-8.6(ology)-313.5(of)-310.4(DPB)-317.4(is)-312.4(as)]TJ 0 -1.0698 TD [(yet)-232.7(unk)-8(nown,)-229.3(A)]TJ 6.974 0 0 6.974 372.756 357.789 Tm 0.0001 Tc [(MIT)71.5(ANI)]TJ /F5 1 Tf 9.963 0 0 9.963 399.458 357.789 Tm 0 Tc [(et)-231.9(al.)]TJ /F4 1 Tf 2.1909 0 TD [([7])-233.1(also)-234.7(sugges)-7.4(ted)-232.7(that)-235.8(one)-230.3(of)]TJ -11.2388 -1.0698 TD [(the)-340.8(aetiologi)-11.5(cal)-335.5(factors)-343(of)-333.2(DPB)-340.2(might)-336.1(be)-337.7(PCD.)]TJ 1.0015 -1.0528 TD -0.0691 Tc [(To)-348.7(t)-69.1(h)-50.3(e)-349.1(a)-69.1(u)-48.3(t)-69.1(h)-55.9(o)-69.1(r)-49.5(s)]TJ /F2 1 Tf 5.6336 0 TD 0 Tc 0 Tw (')Tj /F4 1 Tf 0.4951 0 TD [(kn)15.5(ow)17.3(le)18.5(dg)15.5(e,)-269(th)18.8(is)-266.9(is)-272.6(th)18.9(e)-280(f)0(i)17.3(r)0(s)18.4(t)-276.3(re)13.5(po)21.2(rt)-273(wh)17.3(ic)18.4(h)]TJ -7.1303 -1.0698 TD 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qgd&xh*JUJ.!=NiOYKVT,x}PL'ʧV(T^oJug͵chT@0ꨃFv9[ .`Yg4a u![`,Ɖ A3ox y7mį,^ɲE|9as59/R+c'Фs-wE/wch#7PSSLT iuhUd2H]C Mz93F5BRlمfZ:$ra$mA:`Ϗ͉,Yif=U  h-5ER#=^d!ҷ+$ J^s#>1UIxE6e_)2^Fi Xg!1x%Vx咎 ERJ&;RDf%x؈ޮ}#Pd=F`WtUZU4HUo \jQ|R';+2Q_vH']NazCGUE+ՙZ<8J誧u), 2JCM@zN/*zy*y#ICM%:#/3\6vҾfEo,>?,#x&Jv%O5"(&)ify唻E 0D>&_82^o%h*)(Mjgh J/?x][^N51WU %%LmI̬G 6}8:.Q~SSgE3GYצ}:4E%+-pMɞ9r8}?3qI]VSI!TQe :^=3t0d \O0>D7ēR W__8ѕc&&wI%m] N'eA*EWIdI$r `MNEνqISup|8Lj**i2o,UB I54K-{Hn6 KQs6>`p *lO#Pu3ME[-8ØHN&gYH#+-2;'׉-<Ot5tBRQ=<ܐ5vkN.Qd(`͜jR_# 4P X$Zc-7xԩo$w GU,W,,S>&p2+%dX`E~u' 7fذN H*P3SK(jH]̐ &Y=&yK36 B:xpQ( S8lSdu Z9җeyg~nJQ,ÔꫧdE[NQSD|UW "Hzh2yz:9*&FplφV5GL"jICG 3yQT9aL\3>MzD:ABĸmD&M7FL,T4g~r#󛿔ym){oy|\zh7+LYE_O3xÿV0|DKqGV&7_T|5%Ól`?^O˵~7!Ko2ߤm?=zq{ȾO_|o?{>gEo'~>?B=~߉l*vX7?'G?oÍXVo{~g65rWL?X>t$ݾkmŵ.y#0_>3ǽ ;}FFhOp<]vKyn |c?ʭW> stream BT /F4 1 Tf 9.963 0 0 9.963 58.28 493.228 Tm 0 g /GS2 gs 0 Tc [(patien)-10.1(ts)-272.6(with)-279.2(KS)-277.8(can)-276.2(be)-275.1(divided)-278(into)-281(three)-276.1(kinds)-280.5(of)-276.3(bron-)]TJ 0 -1.0755 TD [(chiolit)-9.6(is:)-389.5(membranou)-9.9(s,)-389.3(obliterat)-13.1(ive)-386.3(and)-389.7(respirato)-11.1(ry)59.5(.)-387.3(Air-)]TJ T* [(flow)-562.9(obstructi)-11.5(on)-553.5(in)-561.6(these)-560.2(patients)-561.5(wi)-7.8(th)-555.9(KS)-556.7(could)-564.3(be)]TJ T* [(deriv)-8.2(ed)-332(from)-339.4(these)-338.2(chan)-9.6(ges)-333.9(of)-333.2(diffuse)-331.2(bronchi)-9.7(olitis)-9.6(.)]TJ 1.0015 -1.0471 TD [(On)-244.5(th)18.9(e)-251.6(o)0(t)18.9(h)0(e)20.8(r)-252.7(ha)15.1(nd)21.2(,)-250.8(h)0(i)18.9(s)0(t)17.7(o)0(p)15.5(a)0(t)18.4(h)0(o)15.5(l)13.9(og)15.5(ic)18.4(al)-243.3(fi)17.3(nd)15.5(i)13.9(n)0(g)15.5(s)-252.3(of)-236.4(th)13.2(e)-245.9(d)0(i)13.2(f)0(-)]TJ -1.0015 -1.0755 TD [(fu)19.6(se)-202.3(ce)20.4(nt)18.9(ri)11.6(l)13.9(o)0(b)15.5(u)0(l)18.9(a)0(r)-202.7(n)0(o)21.2(d)0(u)15.5(l)0(e)18.4(s)-206.8(in)-197.4(DP)18.1(B)-210.3(c)0(o)20.8(r)0(r)12.4(e)0(s)19.6(p)0(o)15.5(n)0(d)21.2(e)0(d)-201.1(t)0(o)-197.4(t)0(h)18.9(o)0(s)20(e)-211.7(of)]TJ T* [(re)19.2(sp)14.4(ir)17.3(at)18.5(or)19.6(y)-336.5(b)0(r)19.6(o)0(n)15.5(c)0(h)20.8(i)0(o)18.9(l)0(i)16.5(t)0(i)16.5(s)0(,)-326.7(w)12.4(hi)13.2(ch)-320.6(sh)14.4(ow)17.3(ed)-320.6(th)18.9(ic)12.8(ke)20.8(ni)18.9(ng)-325.9(of)-321.8(th)13.2(e)]TJ 0 -1.0698 TD [(wa)16.9(ll)16.5(s)-263.7(o)0(f)-253.5(t)13.9(he)-258(re)19.2(sp)20(ir)17.3(at)12.8(or)19.6(y)-262.5(b)0(r)19.6(o)0(n)15.5(c)0(h)20.8(i)0(o)18.9(l)0(i)-256.7(w)0(i)14.9(t)13.9(h)-262.5(i)0(n)18.9(f)0(i)11.6(l)13.9(tr)17.3(at)12.8(io)18.9(n)-262.5(o)0(f)-253.5(l)0(y)18.9(m)0(-)]TJ 0 -1.0755 TD [(ph)15.5(oc)20.8(yt)18.9(es)14(,)-421.5(p)0(l)18.9(a)0(s)13.9(m)0(a)-414.8(c)0(e)20.4(l)0(l)16.5(s)-423.1(an)15.1(d)-421.9(f)0(o)13.9(a)0(m)17.7(y)-421.9(ma)17.7(cr)13.5(op)21.2(ha)15.1(ge)20.8(s)-423.1(w)0(i)14.9(t)0(h)18.9(o)0(u)15.5(t)]TJ T* [(ne)15.1(ut)18.9(ro)19.6(ph)15.5(il)16.5(s)-258(a)0(s)14(s)0(o)20(c)0(i)18.5(a)0(t)18.4(e)0(d)-252.3(w)0(i)14.9(t)0(h)-254.3(s)0(e)19.6(c)0(o)15.1(n)0(d)21.2(a)0(r)13.5(y)-262.5(ec)20.4(ta)18.4(si)17.7(s)-263.7(o)0(f)-253.5(t)0(h)18.9(e)-262.9(pr)19.6(ox)15.5(i-)]TJ 0 -1.0698 TD [(ma)17.7(l)-503.9(m)0(e)17.7(m)0(b)18.1(r)0(a)13.5(n)0(o)21.2(u)0(s)-492.1(b)0(r)19.6(o)0(n)15.5(c)0(h)20.8(i)0(o)13.2(l)0(i)22.2(.)-501.2(Th)17.1(e)-501.9(a)0(l)18.5(v)0(e)15.1(o)0(l)18.9(a)0(r)-492.9(s)0(p)20(a)0(c)14.7(e)0(s)-486.8(w)0(e)11.2(r)0(e)]TJ 0 -1.0755 TD [(ov)15.5(er)19.2(in)18.9(fl)17.3(at)18.4(ed)15.1(,)-250.8(b)0(u)15.5(t)-247.8(wi)14.9(th)18.9(ou)15.5(t)-253.5(e)0(m)17.7(p)0(h)15.5(y)0(s)20(e)0(m)17.7(a)-251.6([1)13.9(6,)-251.5(17].)-266(T)63.4(o)-262.5(demon)-7.4(-)]TJ T* [(strate)-223.5(the)-215.6(differences)-217.5(between)-223.4(KS)-215.2(and)-218.9(DPB,)-215.4(the)-221.3(schemati)-10.7(c)]TJ T* [(recons)-8.2(truction)-464.8(of)-464.1(the)-460.3(bronchioli)-11.1(tis)-457.8(in)-459.2(a)-462.1(case)-460.7(of)-458.4(typi)-7.8(cal)]TJ 25.1977 -1.7584 TD [(DPB)-425.6(is)-420.5(shown)-418.7(in)-419.3(figur)-9.4(e)-416.6(10.)-417.3(The)-6.8(se)-418.5(charact)-10.9(eristic)-425.8(histo-)]TJ 0 -1.0698 TD [(pathol)-9.7(ogical)-243.5(featu)-8.6(res)-244.5(of)-242.1(DPB)-243.5(and)-241.7(the)-244.1(differences)-246(between)]TJ 0 -1.0755 TD [(DPB)-340.2(and)-338.4(OB)-334.5(have)-339.6(been)-333.9(demon)-7.4(stra)-8.6(ted)-335.1(recent)-9.8(ly)-334([18].)]TJ 1.0015 -1.0527 TD [(Th)17.1(us)14.3(,)-376(t)13.9(he)15.1(re)-367.7(we)16.9(re)-367.7(st)17.7(ri)17.3(ki)18.9(ng)-365.7(si)17.7(mi)15.7(la)18.4(ri)17.3(ti)16.5(es)-367.3(be)15.1(tw)20.6(ee)14.7(n)-376.3(K)12.4(S)-375.6(a)0(n)15.1(d)]TJ -1.0015 -1.0755 TD [(DP)12.4(B)-255.9(i)0(n)-254.3(c)0(l)18.4(i)0(n)18.8(i)0(c)18.4(a)0(l)-249(f)0(e)13.5(a)0(t)18.5(u)0(r)19.6(e)0(s)13.9(,)-256.5(ra)19.2(di)13.2(og)21.2(ra)13.5(ph)21.2(y)-256.8(i)0(m)15.7(a)0(g)15.1(e)0(s)-247.8(a)0(n)15.1(d)-256.8(pu)15.5(lm)15.7(on)21.2(-)]TJ T* [(ar)13.5(y)-291(f)0(u)19.6(n)0(c)15.1(t)0(i)16.5(o)0(n)-280.4(t)0(e)18.4(s)0(t)17.7(s)0(;)-283.9(h)0(o)21.2(w)0(e)16.9(v)0(e)15.1(r)37.5(,)-284.9(h)0(i)13.2(s)0(t)17.7(o)0(p)21.2(a)0(t)18.5(h)0(o)15.5(l)0(o)18.9(g)0(i)18.9(c)0(a)14.7(l)-293.4(fe)19.2(at)18.4(ur)13.9(es)-282(ob)21.2(-)]TJ T* [(ta)12.8(in)18.9(ed)-269.4(by)-274.7(re)19.2(co)15.1(ns)20(tr)17.3(uc)15.1(ti)22.2(ng)-274.7(th)18.9(e)-280(l)0(u)13.2(n)0(g)-269(s)0(p)20(e)0(c)14.7(i)0(m)15.7(e)0(n)20.8(s)-280.8(de)15.1(mo)18.1(ns)14.3(t)13.9(r)0(a)13.5(t)0(e)18.4(d)]TJ T* [(di)13.2(st)17.7(in)18.8(ct)-368.5(di)18.9(f)14.7(f)0(e)19.2(r)0(e)19.2(n)0(c)15.1(e)0(s)-367.3(b)0(e)15.1(t)0(w)20.6(e)0(e)14.7(n)-376.3(th)18.9(es)13.9(e)-376.8(t)0(w)14.9(o)-376.3(di)18.9(se)13.9(as)19.6(es)19.6(.)-381.6(T)12.2(he)-371.8(pr)19.6(i-)]TJ 0 -1.0698 TD [(ma)12(ry)-253.5(in)18.9(fl)17.3(am)17.7(ma)17.7(to)13.2(ry)-253.5(l)13.9(e)0(s)13.9(i)0(o)18.9(n)0(s)-253.1(w)0(e)16.9(r)0(e)-253.9(i)0(n)-254.3(t)0(h)18.9(e)-262.9(me)17.7(mb)18.1(ra)13.5(no)21.2(us)-253.1(br)13.9(on)21.2(-)]TJ 0 -1.0755 TD [(ch)15.1(io)18.8(li)-319.3(i)13.9(n)-325.1(KS)-317.7(an)15.1(d)-319.4(i)0(n)-316.9(t)0(h)18.8(e)-325.5(re)19.2(sp)14.4(ir)17.3(at)18.5(or)19.6(y)-325.1(b)0(r)13.9(o)0(n)21.2(c)0(h)15.1(i)0(o)18.9(l)0(i)-313.6(i)0(n)-316.9(D)0(P)18.1(B)0(.)]TJ 1.0015 -1.0528 TD [(Re)16.1(ce)14.7(nt)18.8(ly)81.4(,)-410.1(t)0(h)18.8(e)-410.9(mo)18.1(rt)17.3(al)18.4(it)16.5(y)-410.5(r)0(a)19.2(t)0(e)-397(i)0(n)-402.3(p)0(a)15.1(t)13.9(ie)12.8(nt)18.9(s)-406(w)0(i)14.9(t)0(h)-396.6(D)0(P)12.4(B)-409.5(ha)20.8(s)]TJ -1.0015 -1.0755 TD [(be)15.1(en)-320.6(ma)17.7(rk)19.6(ed)15.1(ly)-316.9(im)15.7(pr)19.6(ov)15.5(ed)-320.6(af)19.2(te)18.4(r)-326.7(t)0(h)13.2(e)-325.5(in)18.8(tr)17.3(od)15.5(uc)20.8(ti)16.5(on)-320.2(of)-316.1(ma)12(cr)19.2(o-)]TJ T* [(li)16.5(de)-212.5(th)18.8(er)19.2(ap)15.1(y)-217(f)0(o)19.6(r)-218.6(DP)12.4(B)-216(i)0(n)-208.8(J)0(a)13.9(p)0(a)20.8(n)-217([1)13.9(9,)-217.4(20].)-231.9(The)-228.7(mecha)-8.2(nism)-231.7(by)]TJ T* [(whi)-8.6(ch)-218.2(macr)-8.6(olide)-219.5(thera)-8.6(py)-217.8(may)-222.1(have)-220.1(a)-223.1(remarkabl)-11.1(e)-217.4(effect)-216.2(on)]TJ 0 -1.0698 TD [(DPB)-436.9(would)-436.9(not)-431.5(be)-428.7(anti)-8.2(bacterial)-438.3(but)-431.5(rathe)-8.6(r)-429.2(anti-inf)-11.2(lam-)]TJ 0 -1.0755 TD [(mat)-8.2(ory)-333.9(effects)-332([21\26123])-8.5(.)]TJ 1.0015 -1.0528 TD [(In)-299(th)18.8(is)-295.3(st)17.7(ud)15.5(y)73.2(,)-307.7(th)18.9(ou)21.2(gh)-297.4(ma)17.7(cr)13.5(ol)18.9(id)18.8(e)-308.5(w)12.4(as)-299(ad)15.1(mi)21.4(ni)13.2(st)17.7(er)19.2(ed)-297.8(to)-294.1(al)18.5(l)]TJ -1.0015 -1.0755 TD [(ei)12.8(gh)21.2(t)-327.5(p)0(a)15.1(t)13.9(ie)12.8(nt)18.9(s)-326.3(w)0(i)14.9(t)13.9(h)-330.8(K)12.4(S,)-319(sp)20(ut)13.2(um)-317.7(vo)21.2(lu)18.9(me)12(,)-324.7(p)0(u)21.2(l)0(m)15.7(o)0(n)15.5(a)0(r)19.2(y)-325.1(fu)13.9(nc)20.8(-)]TJ T* [(ti)16.5(on)-416.9(te)12.8(st)17.7(s)-423.1(a)0(n)15.1(d)-421.9(ra)13.5(di)18.9(og)15.5(ra)19.2(ph)15.5(y)-421.9(i)0(m)15.7(a)0(g)15.1(e)0(s)-418.5(w)12.4(er)13.5(e)-428(n)0(o)21.2(t)-424.2(af)24.9(fe)19.2(ct)12.8(ed)20.8(,)-427.2(a)0(s)]TJ T* [(de)15.1(sc)19.6(ri)17.3(be)15.1(d)-325.1(i)0(n)-316.9(a)-325.5(pr)19.6(ev)15.1(io)18.9(us)-315.7(re)13.5(po)21.2(rt)-318.5([2)19.6(4].)-327.9(Ear)-8.4(ly)-334(antib)-9(iotic)-335.7(ther-)]TJ T* [(apy)54.2(,)-415.8(includ)-9.7(ing)-420.1(quinolone,)-427.8(may)-421.2(be)-423(of)-418.5(benefi)-9.4(t)-418.6(for)-420.9(super-)]TJ 0 -1.0698 TD [(infec)-8.6(tion)-281(and)-281.5(contribut)-10.3(e)-274.3(t)0(o)-277.1(a)-280(favour)-8.2(able)-279.4(prognos)-8.1(is)-278.2(in)-277.1(KS.)]TJ ET 0 0 0 1 k /GS3 gs q 195.6963 0 0 189.9937 68.7416 584.3978 cm /Im8 Do Q BT /F15 1 Tf 9.5 0 0 9.5 221.352 770.833 Tm /GS4 gs (Emphysema)Tj 2.3783 -12.0859 TD -0.06 Tc (LY)Tj -0.0532 -1.989 TD 0 Tc [(L)30(ymphocyte)]TJ 0 -1 TD 0 Tw (plasma cell)Tj -0.3079 -1.8547 TD -0.06 Tc (PA)Tj -9.9828 -1.0187 TD 0 Tc (MB)Tj 0.8 5.1828 TD (RB)Tj -4 4.9094 TD (AD)Tj -5.6719 -9.8626 TD (Neutrophil)Tj 0.0891 4.3719 TD (Dilatation)Tj ET 0 0 0 1 K 0 J 0 j 0.475 w 3.864 M []0 d /GS3 gs 1 i 239.477 765.831 m 206.48 707.109 l 221.68 644.231 m 241.363 655.467 l 230.319 635.073 m 240.843 637.67 l 203.882 609.867 m 235.841 612.792 l 95.597 646.828 m 150.683 642.672 l 111.644 610.195 m 99.13 607.181 l S BT /F4 1 Tf 7.97 0 0 7.97 58.28 572.825 Tm 0 g /GS2 gs [(Fig.)-327.1(6.)-331.2(\261)-332.2(Schematic)-335.5(reconstruction)-339(of)-344.5(the)-343.6(sections)-344(focused)-340.3(on)-344.4(the)-343.6(cen-)]TJ 0 -1.0599 TD [(trilobular)-300.8(lesions)-297.3(of)-301.8(patient)-296.3(7)-303.8(showing)-297.2(the)-300.9(respirator)9.4(y)-303.8(and)-298.6(membranous)]TJ 0 -1.067 TD [(bronchiolitis)-546.9(associated)-544(with)-553.7(peribronc)11.1(hiolar)-553.3(fibrosis)-545.5(\()]TJ /F17 1 Tf 22.9114 0 TD (u)Tj /F4 1 Tf 0.7967 0 TD [(\),)-551.9(fibrohya-)]TJ -23.7081 -1.0599 TD 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