TY - T1的功能性肺动脉高压肺换气不足和更改的影响下的无创性通气JF -欧洲呼吸杂志》乔和J SP - 156 LP - 165欧元——六世- 43 - 1 AU - 10.1183/09031936.00147712马提亚举行Stefan男爵AU - Johanna Walthelm盟盟贝特-克里斯汀·罗斯盟贾妮Y1 - 2014/01/01 UR - //www.qdcxjkg.com/content/43/1/156.abstract N2 -我们协会旨在描述肺动脉高压肺换气不足和运动能力,和无创通气下的血流动力学和功能的变化。进行了回顾性分析,评估血液动力学和功能能力18日间肺动脉高压患者,由于肺换气不足,在基线和3个月后的非侵入式通风。患者伴有平均±sd肺动脉压力的49位±13毫米汞柱,保存心脏指数(3.2±0.66 L·敏−−1·米2),6分钟步行距离303±134 m和严重的氨基端pro-brain利钠肽(中位数水平以上病人)水平升高。平均肺动脉压力和最大工作效率负相关(R = -0.72;p = 0.03)和6分钟步行距离(R = -0.62;p = 0.01)。无创通气后我们发现平均肺动脉压力的显著减少(-18毫米汞柱;术;0.001)和中位数水平以上病人水平(-2110 pg·毫升−1;p = 0.001),改善6分钟步行距离(+ 66;p = 0.008)和最大工作效率(+ 18 W; p=0.028). Changes in work rate correlated inversely with pulmonary artery pressure (R= -0.75; p=0.031). In this specific cohort with hypoventilation and severe pulmonary hypertension, pulmonary hypertension was associated with reduced exercise capacity. Following noninvasive ventilation, haemodynamics and exercise capacity improved significantly. Pulmonary hypertension due to alveolar hypoventilation is associated with functional impairment and improved by NIPPV http://ow.ly/pMYlL ER -