RT Journal第SR电子T1神秘左心血病患者患有肺结乳血管疾病JF欧洲呼吸杂志Jo EUR RESPIR J FD欧洲呼吸学会SP 1083 OP 1091 DO 10.1183 / 09031936.00091212 VO 42是4 A1 FOX,Benjamin D. A1 Shimony188bet官网地址,AVI A1 Langleben,David A1 Hirsch,Andrew A1 Rudski,Robert A1 Schlesinger,Mark J. A1乔森伯格,Dominique A1 Hudson,Marie A1 Boutet,Kim A1 Serban,Alexandrina A1 Masetto,Ariel A1 Baron,Murray YR 2013UL //www.qdcxjkg.com/content/42/4/1083.abstract ab我们的研究旨在确定患有硬皮病和肺动脉高压患者隐匿性左心病的患病率。在肺动脉高压患者中(平均肺动脉压(平均PAP)≥25mmHg),分别根据肺动脉楔压(PAWP)小于或超过15mmHg的毛细血管肺动脉高压和毛细血管后肺动脉高压之间的分化。我们对107例硬皮病患者进行了回顾性图表综述。所有疑似肺动脉高压患者均具有常规或左心导管,左心室舒张压(LVEDP)测量预/后液体攻击。我们提取了人口统计,血管动力学和超声心动图数据。患者分为四组中的一种:血流动力学正常(平均PAP <25 mmHg);肺部静脉高压(​​PVH)(平均PAP≥25mmHg,PAWP> 15 mmHg);神经PVH(平均PAP≥25mmHg,PAWP≤15mmHg,液体挑战前或后15 mmHg);和肺动脉高压(PAH)(平均PAP≥25mmHg,PAWP≤15mmHg和液体攻击前或之后的LVEDP≤15mmHg)。 53 out of 107 patients had pulmonary hypertension. Based on the PAWP-based definition, 29 out of 53 had PAH and 24 out of 53 had PVH. After considering the resting and post-fluid-challenge LVEDP, 11 PAH patients were reclassified as occult PVH. The occult PVH group was haemodynamically, echocardiographically and demographically closer to the PVH group than the PAH group. PVH had high prevalence in our scleroderma-pulmonary hypertension population. Distinguishing PAH from PVH with only PAWP may result in some PVH patients being misclassified as having PAH. Left heart catheterisation with saline infusion helps in the diagnosis of suspected PH in scleroderma http://ow.ly/mxuXE