ty -jour t1-非CF支气管扩张：知道病因会导致管理变化吗？JF-欧洲呼吸杂志JO -EUR RESSIR J SP -8 LP -14 DO -10.1183/09031936.05.00127704 VL -26 IS -1 AU -LI -LI -LI -LI，A.M. AU -SONNAPPA，S.AU -S. AU -LEX，C.AU -WONG -WONG -WONG，C. AU -WONG，C. AU -WONG，C. AU -WONG，E. au -Zacharasiewicz，A.Au -Bush，A.Au -Jaffe，A.Y1-2005/07/01 Ur -http：//www.qdcxjkg.com/content.com/content/26/1/1/8.abstract N2--当前研究的目的是回顾来自两个三级儿科呼吸单元的非囊性纤维化（CF）支气管扩张的病因，以确定使特定的病因诊断的频率导致管理的频率，并评估管理的贡献，并评估计算机断层扫描（CT）在确定基本诊断时。审查了所有被CT诊断为支气管扩张的患者的病例记录，目前在皇家布罗姆普顿医院和大奥蒙德街儿童医院（英国伦敦）看到。所有患者进行了广泛的研究，并记录了潜在的病因和肺部受累区域（如CT所示）。总共确定了136名患者；有65名年轻男性，群体中位数（范围）年龄为12.1岁（3.1-18.1）。免疫缺陷，抽吸和原发性睫毛运动障碍占病例的67％。 In 77 (56%) children, the identification of a cause led to a specific change in management. There was no association between aetiology and the distribution of CT abnormalities. In conclusion, immunodeficiency and other intrinsic abnormalities account for the majority of cases of non-cystic fibrosis bronchiectasis seen in the current authors' units. Computed tomography scans do not contribute towards identifying the aetiology and, most importantly, a specific aetiological diagnosis frequently leads to a change in management. ER -