RT期刊文章SR电子T1慢性血栓栓塞肺动脉高压JF欧洲呼吸杂志Jo EUR RESPIR J FD欧洲呼吸学会SP 2002828 DO 10.1183 / 13993003.02828-2020 VO 57是6 A1 Delcroix,Marion A1 Torbicki,亚当A1 Gopalan188bet官网地址,Deepa A1Sitbon,Olivier A1 Klok,Frederikus A. A1 Lang,Irene A1 Jenkins,David A1 Kim,Nick H. A1 Humbert,Marc A1 Jais,Xavier A1 Vonk Noordegraaf,Anton A1 Brefult,Philippe A1Brénot,彼得A1 Fadel,Elie A1 Ghofrani,Hoossin-Ardeschir A1 Hoper,Marius M. A1 Jansa,Pavel A1 Madani,Michael A1 Matsubara,Hiromi A1 Ogo,TakeShi A1Glünig,Ekkehard A1 D'Armini,Andrea A1 Galie,Nazzareno A1 Meyer,BernhardA1 Corkery,Patrick A1 Meszaros,Gergely A1 Mayer,Eckhard A1 Simonneau,Géraldyr 2021 ul //www.qdcxjkg.com/content/57/6/2002828.abstract ab慢性血栓栓塞肺动脉高压(cteph)是一种罕见的并发症急性肺栓塞,症状或氮ot。纤维化血管内材料近端肺动脉的闭塞,与血管<500μm的次级微血管病变组合,导致肺血管抗性和进步的右心力衰竭增加。负责将红凝块转化为纤维化材料残留的机制尚未阐明。在肺动脉高压患者中,当通风/灌注肺部扫描显示错配灌注缺陷时,怀疑诊断,并通过右心导管和血管成像证实。今天,除了终身抗凝凝血外,治疗方式还包括根据病变的本地化和特征的手术,血管成形术和医疗。本文概述了关于CTEPH诊断和管理的文献和目前实践的审查。它涵盖了急性肺栓塞的定义,诊断,流行病学,患者病理生理学,肺结滴切除术,球囊肺血管成形术,药物及其组合,康复和新的CTH的新研究。它代表了欧洲的第一个合作 Respiratory Society, the International CTEPH Association and the European Reference Network-Lung in the pulmonary hypertension domain. The statement summarises current knowledge, but does not make formal recommendations for clinical practice.The ERS statement on chronic thromboembolic pulmonary hypertension outlines a review of the literature and current practice concerning diagnosis and management of CTEPH https://bit.ly/34dIjot