RT期刊文章SR电子T1生存患者生存患者患者患者相关肺动脉高血压：由国际登记册JF欧洲呼吸期刊JO EUR RESPIR J FD欧洲呼吸学会SP 1901747 DO 10.1183 / 13993003.01747-2019 VO 55是5 A1 Shlobin188bet官网地址，Oksana A. A1 Kouranos，Vasilis A1 Barnett，Scott D. A1 Alhamad，Esam H. A1 Culver，Daniel A. A. A1 Barney，Joseph A1 Cordova，弗朗西斯C. A1 Cormona，Eva M. A1 Scholand，Mary Beth A1 Wijsenbeek，Marlies A1 Ganesh，Sivagini A1 Lower，Elyse E. A1 Engel，Peter J. A1麦芽师，John A1 Price，Laura A1 Wells，athol U. A1 Nathan，Steven D. A1 Baughman，Robert P. YR 2020 UL http：//www.qdcxjkg.com/content/55/5/1901747.Abstract ab引言结节病相关的肺动脉高压（Saph）与单中心研究中的存活率降低有关。建立了长期随访的Saph（退休表）的国际登记处，以丰富我们对这种结节病的并并发症的了解。该分析旨在阐明与Saph患者的无流体存活相关的因素。由于登记登记时间以来，含水患者含有前瞻性收集的Saph患者的结果。分析的信息包括右心导管数据，肺功能测试，胸部射线照相，诈骗阶段和6分钟步行距离（6MWD）。Cox回归模型用于识别无自由移植存活的独立预测因子。结果来自215名患者的数据，然后进行平均±1.9岁以进行分析。在159名前一种患者中，Kaplan-Meier调整的1-，3-和5年的无移植存活分别为89.2％，71.7％和62.0％。事件组的Kaplan-Meier调整后的1-，3-和5年的无移植存活率分别为83.5％，分别为70.3％和58.3％，分别为94.7％，72.2％和66.3％。用于一氧化碳（DLCO）的肺部扩散能力降低的患者（预测的35％）和6MWD <300米在预先群组中的移植存活率显着差。 Reduced 6MWD and preserved forced expiratory volume (FEV1)/forced vital capacity (FVC) ratio were identified as independent risk factors for reduced transplant-free survival in the precapillary cohort.Conclusion Reduced DLCO (<35% pred) and 6MWD (<300 m) at the time of registry enrolment were associated with reduced transplant-free survival in the overall precapillary cohort. Preserved FEV1/FVC ratio was identified as an independent risk factor for worsened outcomes.Decreased 6-min walk distance and reduced diffusion capacity are associated with decreased survival in patients with sarcoidosis-associated pulmonary hypertension http://bit.ly/2UQfWJh