RT期刊文章SR电子T1急性特发性肺纤维化恶化:国际调查,并呼吁协调摩根富林明欧洲呼吸杂志乔和J FD欧元欧洲呼吸学会SP 1901760 10.1183/13993003.01760 -2019签证官55是4 A1迈克尔Kreuter如此说道A1马库斯赶在A1西蒙L.F.沃尔什A1 Johannes Krisam A1哈罗德·r·羽衣甘蓝A1 Nazia乔杜里A1 Ser188bet官网地址geyžA1尤尔根•贝赫A1 Gregory Calligaro A1 Tamera科尔特大学A1凯文Flaherty A1曼Funke-Chambour A1马丁科尔布A1 Yasuhiro Kondoh A1托比·m·马赫A1玛丽亚莫利纳莫利纳A1极其安东尼奥A1 Catharina c .沼泽A1朱莉Morisset A1卡洛斯·佩雷拉A1西尔维亚Quadrelli A1莫伊塞斯塞尔曼A1 Argyrios Tzouvelekis A1克劳迪娅Valenzuela A1卡洛Vancheri A1 Vanesa Vicens-Zygmunt A1茱莉亚拉韦斯。沃尔A1 Wim Wuyts A1土地肥沃的Wijsenbeek A1文森特Cottin A1伊丽莎白Bendstrup年2020 UL //www.qdcxjkg.com/content/55/4/1901760.abstract AB急性恶化的特发性肺纤维化(AE-IPF)是一个经常IPF致命的并发症。没有集中管理国际准则AE-IPF存在。这一国际调查的目的是评估全球变化在预防、诊断和治疗策略AE-IPF。位肺脏与ILD专家被邀请参与一项调查由一个国际专家小组。来自509个国家的66位肺脏回应道。重要的地理变化的方法来管理AE-IPF被发现。常见的预防措施包括antifibrotic药物和疫苗接种。诊断差异最为明显,关于使用克雷布斯·冯·窝Lungen-6和病毒测试,而高分辨率计算机断层扫描、脑利钠肽和肺动脉栓塞通常应用。高剂量类固醇广泛管理(94%);其他免疫抑制剂的使用和治疗策略是高度可变的。很少(4%)急救员从未使用免疫抑制。Antifibrotic治疗期间发起AE-IPF 67%。 Invasive ventilation or extracorporeal membrane oxygenation are mainly used as a bridge to transplantation. Most physicians educate patients comprehensively on the severity of AE-IPF (82%) and consider palliative care (64%).Approaches to the prevention, diagnosis and treatment of AE-IPF vary worldwide. Global trials and guidelines to improve the prognosis of AE-IPF are needed.Lack of focussed international guidelines for management of acute exacerbation of IPF results in global variability in prevention, diagnosis and treatment strategies. Global trials are urgently needed to inform international specific guidelines for AE-IPF. http://bit.ly/3a8FB5i