PT -期刊文章盟Kreuter如此说道,迈克尔盟,赶在马库斯AU -沃尔什,西蒙L.F.盟——Krisam Johannes盟,羽衣甘蓝,哈罗德·r . AU -乔杜里Nazia AU -ž,谢尔盖AU - Behr Jurgen AU - Calligaro,格里高利AU -科尔特大学,Tamera盟,Flaherty Kevin AU - Funke-Chambour曼非盟-科尔布,马丁盟——Kondoh Yasuhiro AU -马赫,托比m . AU -莫利纳莫利纳,玛丽亚AU -莫莱斯,安东尼奥AU -沼泽,Catharina c . AU - Morisset朱莉AU -佩雷拉,卡洛斯AU - Quadrelli,西尔维亚AU -塞尔曼,莫伊塞斯盟——Tzouvelekis Argyrios盟——Valenzuela克劳迪娅AU - Vancheri,卡罗盟——Vicens-Zygmunt Vanesa AU -拉韦斯。沃尔,茱莉亚盟——Wuyts Wim盟——Wijsenbeek土地肥沃的非盟- Cottin,Vincent AU - Bendstrup, Elisabeth TI -特发性肺纤维化急性加重:国际调查,并呼吁协调援助- 10.1183/13993003.01760 -2019 DP - 2020年4月01 TA -欧洲呼吸杂志》第六PG - 1901760 - 55 IP - 4 4099 - //www.qdcxjkg.com/content/55/4/1901760.short 4100 - //www.qdcxjkg.com/content/55/4/1901760.full所以欧元和J2020 4月01;55 AB -特发性肺纤维化急性加重(AE-IPF)通常是IPF的一种致命并发症。目前还没有针对ae -指规数管理的重点国际准则。这项国际调查的目的是评估全球在预防、诊断和治疗策略上的差异。具有肺间质性肺病专家被邀请参加由国际专家组设计的调查。来自66个国家的509名肺科医生做出了回应。在AE-IPF管理方法中发现了显著的地理变异性。常见的预防措施包括抗纤维化药物和疫苗接种。诊断差异在使用克雷伯氏冯登龙根-6和病毒检测方面最为显著，而高分辨率计算机断层扫描、脑利钠肽和d -二聚体通常被应用。 High-dose steroids are widely administered (94%); the use of other immunosuppressant and treatment strategies is highly variable. Very few (4%) responders never use immunosuppression. Antifibrotic treatments are initiated during AE-IPF by 67%. Invasive ventilation or extracorporeal membrane oxygenation are mainly used as a bridge to transplantation. Most physicians educate patients comprehensively on the severity of AE-IPF (82%) and consider palliative care (64%).Approaches to the prevention, diagnosis and treatment of AE-IPF vary worldwide. Global trials and guidelines to improve the prognosis of AE-IPF are needed.Lack of focussed international guidelines for management of acute exacerbation of IPF results in global variability in prevention, diagnosis and treatment strategies. Global trials are urgently needed to inform international specific guidelines for AE-IPF. http://bit.ly/3a8FB5i