TY - T1的特发性肺arterial hypertension with a low diffusing capacity JF - European Respiratory Journal JO - Eur Respir J DO - 10.1183/13993003.00354-2017 VL - 50 IS - 2 SP - 1700354 AU - Olsson, Karen M. AU - Fuge, Jan AU - Meyer, Katrin AU - Welte, Tobias AU - Hoeper, Marius M. Y1 - 2017/08/01 UR - //www.qdcxjkg.com/content/50/2/1700354.abstract N2 - Pulmonary arterial hypertension (PAH) is defined by the presence of pre-capillary pulmonary hypertension (PH) in the absence of underlying causes such as lung diseases, chronic thromboembolic pulmonary hypertension (CTEPH) or other rare conditions [1, 2]. While the idiopathic form of PAH (IPAH) was originally described as a disease affecting primarily younger women [3, 4], it is now increasingly being diagnosed in elderly patients, many of whom present with cardiopulmonary comorbidities, which can make the exact diagnostic classification of such patients difficult [5–8].Elderly patients with IPAH, a smoking history and a low DLCO may suffer from a distinct pulmonary vasculopathy http://ow.ly/sdGh30dxd0G ER -