TY - T1的继发性肺肺泡蛋白质nosis after lung transplantation: a single-centre series JF - European Respiratory Journal JO - Eur Respir J DO - 10.1183/13993003.01369-2016 VL - 49 IS - 2 SP - 1601369 AU - Philippot, Quentin AU - Cazes, Aurélie AU - Borie, Raphaël AU - Debray, Marie-Pierre AU - Danel, Claire AU - Hurtado Nedelec, Maria AU - Boudjemaa, Sabah AU - Sroussi, Déborah AU - Dupin, Clairelyne AU - Mal, Hervé AU - Dauriat, Gaëlle AU - Jean-Baptiste, Sylvain AU - Jebrak, Gilles AU - Castier, Yves AU - Mordant, Pierre AU - Thabut, Gabriel AU - Brugière, Olivier Y1 - 2017/02/01 UR - //www.qdcxjkg.com/content/49/2/1601369.abstract N2 - Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by accumulation of surfactant in alveolar space related to alveolar macrophage dysfunction. PAP occurs in three clinically distinct forms: autoimmune PAP (90% of cases), secondary PAP and genetic PAP [1]. Secondary PAP may be related to immunosuppressive disorders, with few cases associated with solid-organ transplant [1]. Indeed, to our knowledge, only five cases of symptomatic PAP secondary to lung transplantation have been reported [2–4].Pulmonary alveolar proteinosis may occur after lung transplantation and may be a cause of respiratory deterioration http://ow.ly/tlrl307KlKY ER -